Repair or replace? Exploiting novel gene and cell therapy strategies for muscular dystrophies

被引:46
作者
Benedetti, Sara [1 ]
Hoshiya, Hidetoshi [1 ]
Tedesco, Francesco Saverio [1 ,2 ]
机构
[1] UCL, Dept Cell & Dev Biol, London WC1E 6DE, England
[2] Hosp San Raffaele, Div Regenerat Med Stem Cells & Gene Therapy, I-20132 Milan, Italy
基金
英国医学研究理事会; 欧洲研究理事会;
关键词
cell therapy; gene therapy; genome editing; mRNA modifications; muscle regeneration; muscular dystrophy; stem cells; MESENCHYMAL STEM-CELLS; SKELETAL-MUSCLE REGENERATION; TEMPLATE DNA STRANDS; AUTOLOGOUS TRANSPLANTATION; INDUCED PLURIPOTENT; RESTORE DYSTROPHIN; ALPHA-SARCOGLYCAN; SYSTEMIC DELIVERY; IMMUNE-RESPONSES; SATELLITE CELLS;
D O I
10.1111/febs.12178
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
Muscular dystrophies are genetic disorders characterized by skeletal muscle wasting and weakness. Although there is no effective therapy, a number of experimental strategies have been developed over recent years and some of them are undergoing clinical investigation. In this review, we highlight recent developments and key challenges for strategies based upon gene replacement and gene/expression repair, including exon-skipping, vector-mediated gene therapy and cell therapy. Therapeutic strategies for different forms of muscular dystrophy are discussed, with an emphasis on Duchenne muscular dystrophy, given the severity and the relatively advanced status of clinical studies for this disease.
引用
收藏
页码:4263 / 4280
页数:18
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