Hepatocellular carcinoma complicating cystic fibrosis related liver disease

被引:16
作者
O'Donnell, D. H. [1 ,4 ]
Ryan, R. [1 ,4 ]
Hayes, B. [2 ,4 ]
Fennelly, D. [3 ,4 ]
Gibney, R. G. [1 ,4 ]
机构
[1] St Vincents Univ Hosp, Dept Radiol, Dublin 4, Ireland
[2] St Vincents Univ Hosp, Dept Histopathol, Dublin 4, Ireland
[3] St Vincents Univ Hosp, Dept Oncol, Dublin 4, Ireland
[4] St Vincents Univ Hosp, Natl Liver Ctr, Dublin 4, Ireland
关键词
Cystic fibrosis related liver disease; Cirrhosis; Hepatocellular carcinoma; GASTROINTESTINAL MANIFESTATIONS; ULTRASOUND; CIRRHOSIS; DIAGNOSIS;
D O I
10.1016/j.jcf.2009.05.002
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Early diagnosis and treatment of the respiratory and gastrointestinal complications of cystic fibrosis (CF) have led to improved survival with many patients living beyond the fourth decade. Along with this increased life expectancy is the risk of further disease associated with the chronic manifestations of their condition. We report a patient with documented CF related liver disease for which he was under routine surveillance that presented with histologically proven hepatocellular carcinoma (HCC). It is important that physicians are aware of this association as increased vigilance may lead to earlier diagnosis and perhaps, a better outcome. (C) 2009 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.
引用
收藏
页码:288 / 290
页数:3
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