Niemann-Pick disease: a rare problem in anaesthesiological practice

被引：7

作者：

Bujok, LS

Bujok, G

Knapik, P

机构：

[1] Med Univ Silesia, Dept Clin Anaesthesia, PL-41500 Katowice, Poland

[2] Med Univ Silesia, Dept Anaesthesia & Crit Care, Katowice, Poland

[3] Silesian Paediat Ctr, Dept Anaesthesia, Zabrze, Poland

来源：

PAEDIATRIC ANAESTHESIA | 2002年 / 12卷 / 09期

关键词：

Niemann-Pick disease; anaesthesia; difficult intubation;

D O I：

10.1046/j.1460-9592.2002.00922.x

中图分类号：

R614 [麻醉学];

学科分类号：

100217 ;

摘要：

We describe the problems encountered during general anaesthesia in a 2-year-old boy who was suffering from an extremely severe form of Niemann-Pick disease. Attention focused on respiratory difficulties and intubation problems. The usefulness of the lateral position and the limits of the Mallampati score in this case are discussed.

引用

页码：806 / 808

页数：3

共 7 条

[1] Therapy for the sphingolipidoses [J].