Repeat STEP procedure to establish enteral nutrition in an infant with short bowel syndrome
被引:14
作者:
Morikawa, Nobuyuki
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Morikawa, Nobuyuki
[1
]
Kuroda, Tatsuo
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Kuroda, Tatsuo
[1
]
Kitano, Yoshihiro
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Kitano, Yoshihiro
[1
]
Tanaka, Hideaki
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Tanaka, Hideaki
[1
]
Takayasu, Hajime
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Takayasu, Hajime
[1
]
Fujino, Akihiro
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Fujino, Akihiro
[1
]
Shibata, Yumiko
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Shibata, Yumiko
[1
]
Tanemura, Hiroko
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Tanemura, Hiroko
[1
]
Muto, Mitsuru
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Muto, Mitsuru
[1
]
Honna, Toshiro
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Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, JapanNatl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Honna, Toshiro
[1
]
机构:
[1] Natl Ctr Child Hlth & Dev, Div Gen Surg, Setagaya Ku, Tokyo 1578535, Japan
Serial transverse enteroplasty (STEP);
Short bowel syndrome;
Intestinal lengthening;
Bowel dilatation;
Enteral nutrition;
SERIAL TRANSVERSE ENTEROPLASTY;
MITOCHONDRIAL DYSFUNCTION;
LENGTHENING PROCEDURE;
RAT-LIVER;
CHILDREN;
OUTCOMES;
MODEL;
D O I:
10.1007/s00383-009-2456-1
中图分类号:
R72 [儿科学];
学科分类号:
100202 [儿科学];
摘要:
The serial transverse enteroplasty (STEP) procedure is a safe and successful way to lengthen the small bowel in patients with short bowel syndrome. However, postoperative dilatation of the intestine may occur, which induces bacterial overgrowth and malabsorption leading to liver failure. We describe the case of an infant boy with short bowel syndrome caused by jejunal atresia requiring the STEP procedure twice. The first STEP improved the liver function, and the second STEP allowed 80% of the total calorie intake to be tolerated enterally. One should not hesitate to perform a second STEP if after the initial bowel lengthening procedure the patient develops small bowel dilatation that interferes with enteral nutrition.
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Hosp Univ La Paz, Madrid, SpainUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Andres, Ane M.
;
Thompson, Jon
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机构:
Univ Nebraska Med Ctr, Dept Surg, Nebraska Med Ctr, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Thompson, Jon
;
Grant, Wendy
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机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Grant, Wendy
;
Botha, Jean
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机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Botha, Jean
;
Sunderman, Brandy
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机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Sunderman, Brandy
;
Antonson, Dean
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机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Antonson, Dean
;
Langnas, Alan
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机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Langnas, Alan
;
Sudan, Debra
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机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Hosp Univ La Paz, Madrid, SpainUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Andres, Ane M.
;
Thompson, Jon
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nebraska Med Ctr, Dept Surg, Nebraska Med Ctr, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Thompson, Jon
;
Grant, Wendy
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Grant, Wendy
;
Botha, Jean
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Botha, Jean
;
Sunderman, Brandy
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Sunderman, Brandy
;
Antonson, Dean
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Antonson, Dean
;
Langnas, Alan
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA
Langnas, Alan
;
Sudan, Debra
论文数: 0引用数: 0
h-index: 0
机构:
Univ Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USAUniv Nebraska Med Ctr, Dept Surg, Div Solid Organ Transplantat, Omaha, NE 68198 USA