Atypical teratoid/rhabdoid tumors

被引：37

作者：

Dang, T

Vassilyadi, M

Michaud, J

Jimenez, C

Ventureyra, ECG

机构：

[1] Univ Ottawa, Childrens Hosp Eastern Ontario, Div Neurosurg, Ottawa, ON K1H 8L1, Canada

[2] Univ Ottawa, Childrens Hosp Eastern Ontario, Dept Pathol, Ottawa, ON K1H 8L1, Canada

来源：

CHILDS NERVOUS SYSTEM | 2003年 / 19卷 / 04期

关键词：

atypical rhabdoid/teratoid tumor; primitive neuroectodermal tumor medulloblastoma; pediatrics;

D O I：

10.1007/s00381-003-0731-3

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Case reports: We describe three cases of atypical ATRT that were identified at the Children's Hospital of Eastern Ontario. Discussion: Over the past decade, atypical teratoid/rhabdoid tumors (ATRTs) of the central nervous system have emerged as a distinct entity. This tumor is typically misdiagnosed as a primitive neuroectodermal tumor (PNET)/medulloblastoma. The unique immunohistochemistry profile of an ATRT helps distinguish it from a PNET/medulloblastoma. This is of clinical importance because the prognosis of a patient with an ATRT is worse than that of a PNET/medulloblastoma despite Canada aggressive surgical treatment with or without adjuvant chemotherapy and radiation therapy.

引用

页码：244 / 248

页数：5

共 8 条

[1] Central nervous system atypical teratoid/rhabdoid tumors of infancy and childhood [J].