共 88 条
Wnt signaling in polycystic kidney disease
被引:86
作者:

Benzing, Thomas
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Freiburg, Div Renal, D-79106 Freiburg, Germany

Simons, Matias
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Freiburg, Div Renal, D-79106 Freiburg, Germany

Walz, Gerd
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Freiburg, Div Renal, D-79106 Freiburg, Germany
机构:
[1] Univ Hosp Freiburg, Div Renal, D-79106 Freiburg, Germany
[2] Mt Sinai Sch Med, Dept Mol Cell & Dev Biol, New York, NY USA
来源:
JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY
|
2007年
/
18卷
/
05期
关键词:
D O I:
10.1681/ASN.2006121355
中图分类号:
R5 [内科学];
R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号:
1002 ;
100201 ;
摘要:
Wnt signaling cascades activate morphogenetic programs that range from cell migration and proliferation to cell fate determination and stem cell renewal. These pathways enable cells to translate environmental cues into the complex cellular programs that are needed to organize tissues and build organs. Wnt signaling is essential for renal development; however, the specific molecular underpinnings involved are poorly understood. Recent research has revealed an unexpected intersection between Wnt signaling and polycystic kidney disease. Some polycystic kidney disease proteins, such as Inversin and Bardet-Biedl syndrome family members, were found to use components of the Wnt signaling cascade to orient cells along a secondary polarity axis within the plane of the epithelium. These spatial cues may be needed to position nascent tubules with a defined geometry.
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页码:1389 / 1398
页数:10
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