Deterioration of multifocal motor neuropathy after plasma exchange

被引:93
作者
Carpo, M
Cappellari, A
Mora, G
Pedotti, R
Barbieri, S
Scarlato, G
Nobile-Orazio, E
机构
[1] Univ Milan, IRCCS Osped Maggiore Policlin, Ctr Dino Ferrari, Inst Clin Neurol, I-20122 Milan, Italy
[2] Univ Milan, IRCCS Osped Maggiore Policlin, Ctr Dino Ferrari, Giorgio Spagnol Lab Clin Neuroimmunol, I-20122 Milan, Italy
[3] Univ Milan, IRCCS Osped Maggiore Policlin, Ctr Dino Ferrari, Clin Neurophysiol Lab, I-20122 Milan, Italy
[4] IRCCS Fdn Salvatore Maugeri, Ctr Med Veruno, Milan, Italy
关键词
D O I
10.1212/WNL.50.5.1480
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report a patient with motor neuropathy in whom plasma exchange (PE) was followed by a pronounced clinical worsening with the appearance of conduction blocks in previously clinically unaffected motor nerves, leading to the diagnosis of multifocal motor neuropathy (MMN). This report highlights the different response to therapy of MMN and chronic inflammatory demyelinating polyneuropathy (CIDP) because not only steroids but also PE, which is often effective in CIDP, do not improve and at times may even worsen MMN.
引用
收藏
页码:1480 / 1482
页数:3
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