Familial hemiplegic migraine with irreversible brain damage

被引:28
作者
Hayashi, R [1 ]
Tachikawa, H [1 ]
Watanabe, R [1 ]
Honda, M [1 ]
Katsumata, Y [1 ]
机构
[1] Yokohama City Hosp, Dept Neurol, Kanagawa, Japan
关键词
coma; epilepsy; magnetic resonance imaging (MRI); brain atrophy;
D O I
10.2169/internalmedicine.37.166
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Familial hemiplegic migraine (FHM) is an autosomal dominant syndrome characterized by recurrent episodes of varying degrees of hemiparesis associated with migraine. The aura including hemiparesis may be prolonged and in severe attacks may often be associated with confusion or coma, We describe a case of FHM whose aura was atypically prolonged and resulted in irreversible brain deficit which on magnetic resonance imaging (MRI) was suggestive of cortical hyperperfusion. A subsequent MRI showed left brain atrophy.
引用
收藏
页码:166 / 168
页数:3
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