Familial Mediterranean fever: The genetics of inflammation

被引：58

作者：

Kastner, DL ^{[1
]}

机构：

[1] NIAMSD, Genet Sect, Arthrit & Rheumatism Branch, Bethesda, MD 20892 USA

来源：

HOSPITAL PRACTICE | 1998年 / 33卷 / 04期

关键词：

D O I：

10.3810/hp.1998.04.90

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

When a patient complains of episodic fever accompanied by unexplained arthritis, peritonitis, pleurisy, or skin rash, this disorder should be considered. The disease-related gene codes for a protein that guides a neutrophil's participation in inflammation; the protein's existence implies an entire regulatory pathway hitherto unknown. At least two other mendelian periodic fever syndromes have also been described.

引用

页码：131 / +

页数：14

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