The remarkable right ventricle of patients with Eisenmenger syndrome

被引:109
作者
Hopkins, WE [1 ]
机构
[1] Univ Vermont, Coll Med, Cardiol Unit, Burlington, VT 05401 USA
关键词
Eisenmenger syndrome; pulmonary hypertension; congenital heart disease; adult;
D O I
10.1097/00019501-200502000-00004
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Patients with Eisenmenger syndrome do much better than patients with all other etiologies of severe pulmonary hypertension. The primary reason, and a major focus of this review, is the right ventricle, a remarkable chamber with preserved systolic function despite a lifetime of systemic level pulmonary hypertension. (C) 2005 Lippincott Williams Wilkins.
引用
收藏
页码:19 / 25
页数:7
相关论文
共 19 条
[1]   Continuous intravenous epoprostenol for pulmonary hypertension due to the scleroderma spectrum of disease -: A randomized, controlled trial [J].
Badesch, DB ;
Tapson, VF ;
McGoon, MD ;
Brundage, BH ;
Rubin, LJ ;
Wigley, FM ;
Rich, S ;
Barst, RJ ;
Barrett, PS ;
Kral, KM ;
Jöbsis, MM ;
Loyd, JE ;
Murali, S ;
Frost, A ;
Girgis, R ;
Bourge, RC ;
Ralph, DD ;
Elliott, CG ;
Hill, NS ;
Langleben, D ;
Schilz, RJ ;
McLaughlin, VV ;
Robbins, IM ;
Groves, BM ;
Shapiro, S ;
Medsger, TA ;
Gaine, SP ;
Horn, E ;
Decker, JC ;
Knobil, K .
ANNALS OF INTERNAL MEDICINE, 2000, 132 (06) :425-+
[2]   SURVIVAL IN PATIENTS WITH PRIMARY PULMONARY-HYPERTENSION - RESULTS FROM A NATIONAL PROSPECTIVE REGISTRY [J].
DALONZO, GE ;
BARST, RJ ;
AYRES, SM ;
BERGOFSKY, EH ;
BRUNDAGE, BH ;
DETRE, KM ;
FISHMAN, AP ;
GOLDRING, RM ;
GROVES, BM ;
KERNIS, JT ;
LEVY, PS ;
PIETRA, GG ;
REID, LM ;
REEVES, JT ;
RICH, S ;
VREIM, CE ;
WILLIAMS, GW ;
WU, M .
ANNALS OF INTERNAL MEDICINE, 1991, 115 (05) :343-349
[3]   PRIMARY PULMONARY-HYPERTENSION - NATURAL-HISTORY AND THE IMPORTANCE OF THROMBOSIS [J].
FUSTER, V ;
STEELE, PM ;
EDWARDS, WD ;
GERSH, BJ ;
MCGOON, MD ;
FRYE, RL .
CIRCULATION, 1984, 70 (04) :580-587
[4]  
Hopkins WE, 1996, J HEART LUNG TRANSPL, V15, P100
[5]  
Hopkins WE, 1999, CLIN G MED MANAG, P581
[6]   Severe pulmonary hypertension without right ventricular failure: The unique hearts of patients with Eisenmenger syndrome [J].
Hopkins, WE ;
Waggoner, AD .
AMERICAN JOURNAL OF CARDIOLOGY, 2002, 89 (01) :34-38
[7]  
HOPKINS WE, 1995, CURR OPIN CARDIOL, V10, P517, DOI 10.1097/00001573-199509000-00014
[8]   Eisenmenger syndrome in adults: Ventricular septal defect, truncus arteriosus, univentricular heart [J].
Niwa, K ;
Perloff, JK ;
Kaplan, S ;
Child, JS ;
Miner, PD .
JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1999, 34 (01) :223-232
[9]  
PERLOFF JK, 1998, CONGENITAL HEART DIS, P199
[10]  
Rich S, 2001, HEART DIS TXB CARDIO, P1908