Abdominal situs inversus with congenital duodenal stenosis: Rare association

被引:7
作者
Akel, S
Halabi, J
Shawis, R
机构
[1] Amer Univ Beirut, Dept Surg, Med Ctr, Beirut, Lebanon
[2] Tawam Hosp, Al Ain, U Arab Emirates
关键词
abdominal situs inversus; isolated levocardia; abdominal heterotaxia; duodenal obstruction;
D O I
10.1055/s-2008-1071120
中图分类号
R72 [儿科学];
学科分类号
100202 [儿科学];
摘要
Abdominal situs inversus carries a significant mortality because the majority of cases (95 %) have associated cardiac and splenic defects (9). A review of all cases reported in the English literature confirms in addition the presence of significant gastro-intestinal pathologies, mainly annular pancreas, midgut volvulus and duodenal atresia. We report on an additional case of abdominal situs inversus without cardiac or splenic abnormalities, who had partial duodenal obstruction secondary to a mucosal diaphragm. This seems to be the thirteenth case associated with duodenal obstruction and the sixth case secondary to a mucosal duodenal diaphragm, to date, in this setting (1, 2, 3, 4, 5, 7).
引用
收藏
页码:55 / 57
页数:3
相关论文
共 11 条
[2]
INTESTINAL ROTATION AND FIXATION ABNORMALITIES IN HETEROTAXIA - EARLY DETECTION AND MANAGEMENT [J].
CHANG, J ;
BRUECKNER, M ;
TOULOUKIAN, RJ .
JOURNAL OF PEDIATRIC SURGERY, 1993, 28 (10) :1281-1285
[3]
DAVENPORT M, 1993, SURGERY, V113, P662
[4]
FONKALSRUD EW, 1966, ARCH SURG-CHICAGO, V92, P791
[5]
IUCHTMAN M, 1993, AM J PERINAT, V10, P255
[6]
LOSA M, 1995, EUR J PEDIATR, V154, P236
[7]
SITUS INVERSUS - THE COMPLEX INDUCING NEONATAL INTESTINAL-OBSTRUCTION [J].
RUBEN, GD ;
TEMPLETON, JM ;
ZIEGLER, MM .
JOURNAL OF PEDIATRIC SURGERY, 1983, 18 (06) :751-756
[8]
A CASE OF AGNATHIA, SITUS-INVERSUS, AND A NORMAL CENTRAL-NERVOUS-SYSTEM [J].
STOLER, JM ;
HOLMES, LB .
TERATOLOGY, 1992, 46 (03) :213-216
[9]
PARTIAL SITUS-INVERSUS - DUODENAL OBSTRUCTION IN A NEONATE WITH ISOLATED LEVOCARDIA [J].
TRYFONAS, GI ;
CHAIDOS, C ;
AVTZOGLOU, PP ;
ZIOUTIS, J ;
KLOKARIS, A ;
PAPANASTASOPOULOS, A .
JOURNAL OF PEDIATRIC SURGERY, 1992, 27 (12) :1584-1586
[10]
BILIARY ATRESIA AND THE POLYSPLENIA SYNDROME - ITS IMPACT ON FINAL OUTCOME [J].
VAZQUEZ, J ;
GUTIERREZ, JCL ;
GAMEZ, M ;
LOPEZSANTAMARIA, M ;
MURCIA, J ;
LARRAURI, J ;
DIAZ, MC ;
JARA, P ;
TOVAR, JA .
JOURNAL OF PEDIATRIC SURGERY, 1995, 30 (03) :485-487