Dethroning the myth: Cognitive dissociations and innate modularity in Williams syndrome

被引:91
作者
Karmiloff-Smith, A [1 ]
Brown, JH [1 ]
Grice, S [1 ]
Paterson, S [1 ]
机构
[1] Inst Child Hlth, Neurocognit Dev Unit, London WC1N 1EH, England
关键词
D O I
10.1207/S15326942DN231&2_10
中图分类号
B844 [发展心理学(人类心理学)];
学科分类号
040202 ;
摘要
Despite increasing empirical data to the contrary, it continues to be claimed that morphosyntax and face processing skills of people with Williams syndrome are intact, This purported intactness, which coexists with mental retardation, is used to bolster claims about innately specified, independently functioning modules, as if the atypically developing brain were simply a normal brain with parts intact and parts impaired. Yet this is highly unlikely, given the dynamics of brain development and the fact that in a genetic microdeletion syndrome the brain is developing differently from the moment of conception, throughout embryogenesis, and during postnatal brain growth. In this article, we challenge the intactness assumptions, using evidence from a wide variety of studies of toddlers, children, and adults with Williams syndrome.
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收藏
页码:227 / 242
页数:16
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