Clinical aspects of Langerhans cell histiocytosis

被引:118
作者
Aricò, M
Egeler, RM
机构
[1] Univ Pavia, Dept Pediat, IRCCS, Policlin San Matteo, I-27100 Pavia, Italy
[2] Univ Calgary, Tom Baker Canc Ctr, Alberta Childrens Hosp, So Alberta Childrens Canc Program, Calgary, AB, Canada
[3] Erasmus Univ, Sophia Childrens Hosp, Div Pediat Oncol, Rotterdam, Netherlands
关键词
D O I
10.1016/S0889-8588(05)70508-6
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Langerhans cell histiocytosis remains an enigmatic disease with protean manifestations. It may be self-limited in some, whereas in others, even intensive treatment is unsuccessful. The outcome depends on whether vital organ function is compromised at diagnosis or shortly thereafter, in which case the prognosis is grave.
引用
收藏
页码:247 / +
页数:13
相关论文
共 75 条
[1]  
ARICO M, 1996, MED PEDIATR ONCOL, V27, P575
[2]  
ARICO M, 1996, MED PEDIATR ONCOL, V27, P580
[3]  
AXIOTIS CA, 1991, CANCER-AM CANCER SOC, V67, P1650, DOI 10.1002/1097-0142(19910315)67:6<1650::AID-CNCR2820670629>3.0.CO
[4]  
2-T
[5]   Restricted catch-up growth after cessation of steroid treatment in a growth-hormone-deficient child [J].
Boersma, B ;
Wit, JM .
ACTA PAEDIATRICA, 1996, 85 (08) :998-1002
[6]   RUPTURED SPLEEN AS A CAUSE OF DEATH IN AN INFANT WITH LANGERHANS CELL HISTIOCYTOSIS (HISTIOCYTOSIS-X) [J].
BROADBENT, V ;
WILLIAMS, M ;
DOSSETOR, J .
PEDIATRIC HEMATOLOGY AND ONCOLOGY, 1990, 7 (03) :297-299
[7]  
Broadbent V, 1997, MED PEDIATR ONCOL, V28, P289, DOI 10.1002/(SICI)1096-911X(199704)28:4<289::AID-MPO8>3.0.CO
[8]  
2-E
[9]   HISTIOCYTOSIS SYNDROMES IN CHILDREN .2. APPROACH TO THE CLINICAL AND LABORATORY EVALUATION OF CHILDREN WITH LANGERHANS CELL HISTIOCYTOSIS [J].
BROADBENT, V ;
GADNER, H ;
KOMP, DM ;
LADISCH, S .
MEDICAL AND PEDIATRIC ONCOLOGY, 1989, 17 (06) :492-495
[10]   ANTERIOR-PITUITARY FUNCTION AND COMPUTED-TOMOGRAPHY MAGNETIC-RESONANCE-IMAGING IN PATIENTS WITH LANGERHANS CELL HISTIOCYTOSIS AND DIABETES-INSIPIDUS [J].
BROADBENT, V ;
DUNGER, DB ;
YEOMANS, E ;
KENDALL, B .
MEDICAL AND PEDIATRIC ONCOLOGY, 1993, 21 (09) :649-654