Developmental dysplasia of the hip in Marfan syndrome

被引：11

作者：

Sponseller, PD

Tomek, IM

Pyertiz, RE

机构：

[1] Department of Orthopaedic Surgery, Johns Hopkins University, Baltimore, MD

[2] Department of Human Genetics, Allegheny-Singer Research Institute, Pittsburgh, PA

[3] Department of Orthopaedic Surgery, Johns Hopkins Outpatient Centre, Baltimore, MD 21287-0882

来源：

JOURNAL OF PEDIATRIC ORTHOPAEDICS-PART B | 1997年 / 6卷 / 04期

关键词：

developmental dysplasia; Marfan syndrome;

D O I：

10.1097/01202412-199710000-00007

中图分类号：

R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学（修复外科学）];

学科分类号：

摘要：

Among 235 consecutive patients with Marfan syn drome, four cases of developmental dysplasia of the hip were found, amounting to an incidence of 2%. Harness treatment was not effective in any of the patients because of a narrow stable zone and knee laxity. One patient died of cardiac failure before further treatment could be attempted. Closed reduction and spica cast treatment was successful in all other patients. Stability was achieved within a normal period, and there were no redislocations. Consequently, the dislocated hip in patients with Marfan syndrome should be managed early with this method.

引用

页码：255 / 259

页数：5

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