The hereditary autoinflammatory syndromes

被引：13

作者：

Chitkara, Puja ^{[1
]}

Stojanov, Silvia ^{[1
]}

Kastner, Daniel L. ^{[1
]}

机构：

[1] NIAMSD, NIH, Bethesda, MD 20892 USA

来源：

PEDIATRIC INFECTIOUS DISEASE JOURNAL | 2007年 / 26卷 / 04期

关键词：

recurrent fever; hereditary autoinflammatory syndromes; tumor necrosis factor; periodic fever syndromes;

D O I：

10.1097/01.inf.0000258777.86510.da

中图分类号：

R392 [医学免疫学]; Q939.91 [免疫学];

学科分类号：

100102 [免疫学];

摘要：

Although most recurrent fevers in children are due to frequent viral and/or bacterial infections, in those who have periodic fevers without clear etiology, the clinician should consider the hereditary autoinflammatory syndromes. These rare syndromes are characterized by recurrent episodes of seemingly unprovoked inflammation. They are a unique group of diseases with permanent genetic defects but intermittent clinical manifestations. Systemic amyloidosis is the major complication for some of these disorders. Copyright © 2007 by Lippincott Williams & Wilkins.

引用

页码：353 / 354

页数：2

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