Primary cutaneous Ewing's sarcoma/primitive neuroectodermal tumor manifesting numerous small and huge ulcerated masses: its complete remission by chemotherapy and magnetic resonance imaging findings

被引:10
作者
Bahk, Won-Jong [1 ]
Chang, Eun-Deok [2 ]
Bae, Jung Min [3 ]
Chun, Kyung-Ah [4 ]
Lee, An-Hee [2 ]
Rho, Sang-Young [5 ]
Kim, Jin Woo [3 ]
机构
[1] Catholic Univ Korea, Uijeongbu St Marys Hosp, Dept Orthoped Surg, Uijongbu, South Korea
[2] Catholic Univ Korea, Uijeongbu St Marys Hosp, Dept Pathol, Uijongbu, South Korea
[3] Catholic Univ Korea, Uijeongbu St Marys Hosp, Dept Dermatol, Uijongbu, South Korea
[4] Catholic Univ Korea, Uijeongbu St Marys Hosp, Dept Radiol, Uijongbu, South Korea
[5] Catholic Univ Korea, Uijeongbu St Marys Hosp, Dept Hematooncol, Uijongbu, South Korea
关键词
Primary cutaneous Ewing's sarcoma/primitive neuroectodermal tumor; MRI findings; Multiple huge masses; Clinical outcome; SARCOMA; P30/32(MIC2); DIAGNOSIS;
D O I
10.1007/s00256-009-0872-x
中图分类号
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学(修复外科学)];
学科分类号
100224 [整形外科学];
摘要
Extraskeletal Ewing's sarcoma (ES) and primitive neuroectodermal tumor (PNET) are widely regarded as clinically and histologically identical tumors which consist of small blue round cells. Extraskeletal ESs/PNETs usually occur in the deep soft tissues of the paraspinal region, chest wall, or lower extremities. However, superficially located cases, so-called cutaneous ESs/PNETs, are exceedingly rare, and the vast majority of the reported cases present as a single small mass. We present magnetic resonance imaging (MRI) findings and clinical course of a unique case of primary cutaneous ES/PNET presenting as numerous huge masses with severe ulceration on them.
引用
收藏
页码:595 / 600
页数:6
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