Quantitative Western blot analysis of plasma ADAMTS13 antigen in patients with Upshaw-Schulman syndrome

被引：11

作者：

Ishizashi, Hiromichi

Yagi, Hideo

Matsumoto, Masanori

Soejima, Kenji

Nakagaki, Tomohiro

Fujimura, Yoshihiro

机构：

[1] Nara Med Univ, Dept Blood Transfus Med, Kashihara, Nara 6348522, Japan

[2] Nara Med Univ, Dept Blood Transfus Med, Kashihara, Nara 6348522, Japan

[3] Chemosero Therapeut Res Inst, Res Dept 1, Kumamoto 8691298, Japan

来源：

THROMBOSIS RESEARCH | 2007年 / 120卷 / 03期

关键词：

ADAMTS13; antigen; USS; TTP;

D O I：

10.1016/j.thromres.2006.07.012

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

[No abstract available]

引用

页码：381 / 386

页数：6

共 24 条

[1] THROMBOTIC THROMBOCYTOPENIC PURPURA - REPORT OF 16 CASES AND REVIEW OF LITERATURE [J].

AMOROSI, EL ;

ULTMANN, JE .

MEDICINE, 1966, 45 (02) :139-+

[2] ADAMTS13 gene defects in two brothers with constitutional thrombotic thrombocytopenic purpura and normalization of von Willebrand factor-cleaving protease activity by recombinant human ADAMTS13 [J].

Antoine, G ;

Zimmermann, K ;

Plaimauer, B ;

Grillowitzer, M ;

Studt, JD ;

Lämmle, B ;

Scheiflinger, F .

BRITISH JOURNAL OF HAEMATOLOGY, 2003, 120 (05) :821-824

[3] Ten years of prophylactic treatment with fresh-frozen plasma in a child with chronic relapsing thrombotic thrombocytopenic purpura as a result of a congenital deficiency of von Willebrand factor-cleaving protease [J].

Barbot, J ;

Costa, E ;

Guerra, M ;

Barreirinho, MS ;

Isvarlal, P ;

Robles, R ;

Gerritsen, HE ;

Lämmle, B ;

Furlan, M .

BRITISH JOURNAL OF HAEMATOLOGY, 2001, 113 (03) :649-651

[4] Proteolytic inactivation of ADAMTS13 by thrombin and plasmin [J].

Crawley, JTB ;

Lam, JK ;

Rance, JB ;

Mollica, LR ;

O'Donnell, JS ;

Lane, DA .

BLOOD, 2005, 105 (03) :1085-1093

[5] ADAMTS-13 plasma level determination uncovers antigen absence in acquired thrombotic thrombocytopenic purpura and ethnic differences [J].

Feys, HB ;

Liu, F ;

Dong, N ;

Pareyn, I ;

Vauterin, S ;

Vandeputte, N ;

Noppe, W ;

Ruan, C ;

Deckmyn, H ;

Vanhoorelbeke, K .

JOURNAL OF THROMBOSIS AND HAEMOSTASIS, 2006, 4 (05) :955-962

[6] Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura [J].

Furlan, M ;

Robles, R ;

Solenthaler, M ;

Wassmer, M ;

Sandoz, P ;

Lammle, B .

BLOOD, 1997, 89 (09) :3097-3103

[7] New strategies in diagnosis and treatment of thrombotic thrombocytopenic purpura:: case report and review [J].

Häberle, J ;

Kehrel, B ;

Ritter, J ;

Jürgens, H ;

Lämmle, B ;

Furlan, M .

EUROPEAN JOURNAL OF PEDIATRICS, 1999, 158 (11) :883-887

[8] Novel monoclonal antibody-based enzyme immunoassay for determining plasma levels of ADAMTS13 activity [J].

Kato, Seiji ;

Matsumoto, Masanori ;

Matsuyama, Tomomi ;

Isonishi, Ayami ;

Hiura, Hisahide ;

Fujimura, Yoshihiro .

TRANSFUSION, 2006, 46 (08) :1444-1452

[9] Upshaw-Schulman syndrome revisited: A concept of congenital thrombotic thrombocytopenic purpura [J].

Kinoshita, S ;

Yoshioka, A ;

Park, YD ;

Ishizashi, H ;

Konno, M ;

Funato, M ;

Matsui, T ;

Titani, K ;

Yagi, H ;

Matsumoto, M ;

Fujimura, Y .

INTERNATIONAL JOURNAL OF HEMATOLOGY, 2001, 74 (01) :101-108

[10] Mutations and common polymorphisms in ADAMTS13 gene responsiblefor von Willebrand factor-cleaving protease activity [J].

Kokame, K ;

Matsumoto, M ;

Soejima, K ;

Yagi, H ;

Ishizashi, H ;

Funato, M ;

Tamai, H ;

Konno, M ;

Kamide, K ;

Kawano, Y ;

Miyata, T ;

Fujimura, Y .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2002, 99 (18) :11902-11907

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