Ventricular dysfunction and number of non compacted segments in non compaction: Non-independent predictors

被引:20
作者
Fazio, Giovanni [1 ]
Corrado, Giovanni [2 ]
Novo, Giuseppina [1 ]
Zachara, Elisabetta [5 ]
Rapezzi, Claudio [3 ,4 ]
Sulafa, Ali K. [6 ]
Sutera, Loredana [1 ]
D'angelo, Luciana [1 ]
Visconti, Claudia [1 ]
Stollberger, Claudia [7 ]
Sormani, Luca [2 ]
Finsterer, Joseph [9 ]
Cavusoglu, Yuksel [10 ]
Di Gesaro, Gabriele [1 ]
Grassedonio, Emanuele [8 ]
Ferrara, Filippo [1 ]
Galia, Massino [8 ]
Midiri, Massimo [8 ]
Pipitone, Salvatore [11 ]
Carerj, Scipione [12 ]
Novo, Salvatore [1 ]
机构
[1] Univ Palermo, Dept Cardiol, I-90133 Palermo, Italy
[2] Valduce Hosp, Dept Cardiol, Como, Italy
[3] Univ Bologna, Inst Cardiol, Bologna, Italy
[4] St Orsola Marcello Malpighi Hosp, Bologna, Italy
[5] S Camillo Forlanini Hosp, Div Cardiol 2, Rome, Italy
[6] Div Pediat Cardiol, Riyadh, Saudi Arabia
[7] Krankenanstalt, Dept Med 2, Vienna, Austria
[8] Univ Palermo, Dept Radiol, I-90133 Palermo, Italy
[9] Krankenanstalt Rudolfstiftung Wien, Vienna, Austria
[10] Osmangazi Univ, Dept Cardiol, Eskisehir, Turkey
[11] Casa Sole Hosp, Div Cardiol, Palermo, Italy
[12] Univ Messina, Dept Cardiol, I-98100 Messina, Italy
关键词
Ventricular non compaction; Cardiomyopathy; Ventricular dysfunction; Number of segments; Compact/spongy ratio; ISOLATED NONCOMPACTION; FREQUENT COMPLICATION; BARTH-SYNDROME; HEART-FAILURE; MYOCARDIUM; CARDIOMYOPATHY; DIAGNOSIS; ADULTS; ECHOCARDIOGRAPHY; TACHYCARDIA;
D O I
10.1016/j.ijcard.2008.11.199
中图分类号
R5 [内科学];
学科分类号
100201 [内科学];
摘要
Background: Isolated ventricular noncompaction (IVNC) is characterized by multiple prominent trabeculations and deep intertrabecular recesses. Some reports prove that the chronic heart failure may occur in approximately half of the patients. In this report we investigate the correlation between the number of non compacted segments and entity of systolic dysfunction from the registry and subregistries of the SIEC. Method: To identify the correlation between ventricular dysfunction and number of segments involved in non compaction we evaluated a consecutive series of 238 patients affected by non compaction, from the SIEC (Societa Italiana di Ecografia Cardiovascolare) registry. The average age of patients was 41.5 years (range: 1-92 years), 137 were males and 101 females. In 122 cases we found ventricular systolic dysfunctions with an EF average of 34.6%. The number of affected segments by non-compactation and diastolic dysfunction were found to be non-independent predictors of LV systolic dysfunction. Conclusion: From the analyses we carried out, it seems that ventricular dysfunction seems to be completely independent from the segment numbers of non compacted segments. (c) 2009 Elsevier Ireland Ltd. All rights reserved.
引用
收藏
页码:250 / 253
页数:4
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