Retroperitoneal lymphangioleiomyomatosis: CT appearance

被引:9
作者
Kehagias, D
Pafiti, A
Vaos, N
Samanidis, L
机构
[1] Univ Athens, Areteion Hosp, Dept Radiol, Athens 11528, Greece
[2] Areteion Hosp, Dept Pathol, Athens, Greece
[3] Areteion Hosp, Dept Surg, Athens, Greece
关键词
lymphangioleiomyomatosis; retroperitoneum; computed tomography;
D O I
10.1007/s003300050417
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 [临床医学]; 100207 [影像医学与核医学]; 1009 [特种医学];
摘要
Lymphangioleiomyomatosis is a rare disease involving the lung, lymphatic trunk and lymph nodes. Sometimes it appears in the retroperitoneum with or without subsequent development in the lungs. We present a 52-year-old woman with retroperitoneal location of the disease. We discuss the abdominal CT appearance, the cytologic and immunophenotypic features and a preoperative differential diagnosis is attempted.
引用
收藏
页码:471 / 473
页数:3
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