Polyglutamine-containing aggregates in neuronal intranuclear inclusion disease

被引:48
作者
Lieberman, AP [1 ]
Robitaille, Y
Trojanowski, JQ
Dickson, DW
Fischbeck, KH
机构
[1] Univ Penn, Sch Med, Dept Pathol & Lab Med, Philadelphia, PA 19104 USA
[2] Univ Penn, Sch Med, Dept Neurol, Philadelphia, PA 19104 USA
[3] McGill Univ, Dept Neurol & Neurosurg, Montreal, PQ, Canada
[4] Univ Montreal, Dept Pathol, Montreal, PQ H3C 3J7, Canada
[5] Mayo Clin Jacksonville, Jacksonville, FL 32224 USA
基金
美国国家卫生研究院;
关键词
D O I
10.1016/S0140-6736(05)70296-8
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:884 / 884
页数:1
相关论文
共 5 条
[1]   NEURONAL INTRANUCLEAR INCLUSION DISEASE IN IDENTICAL-TWINS [J].
HALTIA, M ;
SOMER, H ;
PALO, J ;
JOHNSON, WG .
ANNALS OF NEUROLOGY, 1984, 15 (04) :316-321
[2]   Polyglutamines, nuclear inclusions and neurodegeneration [J].
Lunkes, A ;
Mandel, JL .
NATURE MEDICINE, 1997, 3 (11) :1201-1202
[3]   ADULT-ONSET NEURONAL INTRANUCLEAR HYALINE INCLUSION DISEASE [J].
MUNOZGARCIA, D ;
LUDWIN, SK .
NEUROLOGY, 1986, 36 (06) :785-790
[4]  
SCHUFFLER MD, 1978, GASTROENTEROLOGY, V75, P889
[5]   POLYGLUTAMINE EXPANSION AS A PATHOLOGICAL EPITOPE IN HUNTINGTONS-DISEASE AND 4 DOMINANT CEREBELLAR ATAXIAS [J].
TROTTIER, Y ;
LUTZ, Y ;
STEVANIN, G ;
IMBERT, G ;
DEVYS, D ;
CANCEL, G ;
SAUDOU, F ;
WEBER, C ;
DAVID, G ;
TORA, L ;
AGID, Y ;
BRICE, A ;
MANDEL, JL .
NATURE, 1995, 378 (6555) :403-406