Modern management of severe platelet function disorders

被引：61

作者：

Alamelu, Jayanthi ^{[1
]}

Liesner, Ri ^{[2
]}

机构：

[1] Guys & St Thomas Hosp, Dept Thrombosis & Haemostasis, London SE1 7EH, England

[2] Great Ormond St Hosp Sick Children, Dept Thrombosis & Haemostasis, London, England

来源：

BRITISH JOURNAL OF HAEMATOLOGY | 2010年 / 149卷 / 06期

关键词：

platelet function disorders; Glanzmann Thrombasthenia; Bernard-Soulier Syndrome; BERNARD-SOULIER-SYNDROME; RECOMBINANT FACTOR-VIIA; BONE-MARROW-TRANSPLANTATION; STEM-CELL TRANSPLANTATION; GLYCOPROTEIN-IB-ALPHA; OF-THE-LITERATURE; HERMANSKY-PUDLAK-SYNDROME; STORAGE-POOL-DISEASE; GLANZMANNS-THROMBASTHENIA; BLEEDING DISORDERS;

D O I：

10.1111/j.1365-2141.2010.08191.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

P>Severe platelet function defects are rare disorders that require expertise in diagnosis and management. Therefore patients with such disorders should be referred to and managed in centres with the full laboratory repertoire of tests and clinical support necessary to optimise their quality of care. The aim of this review is to discuss the management of these patients in various clinical situations including surgical intervention.

引用

页码：813 / 823

页数：11

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