学术探索
学术期刊
新闻热点
数据分析
智能评审
立即登录
Cystic fibrosis
被引:150
作者
:
Rosenstein, BJ
论文数:
0
引用数:
0
h-index:
0
机构:
Johns Hopkins Univ, Sch Med, Baltimore, MD USA
Johns Hopkins Univ, Sch Med, Baltimore, MD USA
Rosenstein, BJ
[
1
]
Zeitlin, PL
论文数:
0
引用数:
0
h-index:
0
机构:
Johns Hopkins Univ, Sch Med, Baltimore, MD USA
Johns Hopkins Univ, Sch Med, Baltimore, MD USA
Zeitlin, PL
[
1
]
机构
:
[1]
Johns Hopkins Univ, Sch Med, Baltimore, MD USA
来源
:
LANCET
|
1998年
/ 351卷
/ 9098期
关键词
:
D O I
:
10.1016/S0140-6736(97)09174-5
中图分类号
:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
摘要
:
[No abstract available]
引用
收藏
页码:277 / 282
页数:6
相关论文
共 83 条
[1]
ALTON EWFW, 1990, EUR RESPIR J, V3, P922
[2]
The effects of panresistant bacteria in cystic fibrosis patients on lung transplant outcome
[J].
Aris, RM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Aris, RM
;
Gilligan, PH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Gilligan, PH
;
Neuringer, IP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Neuringer, IP
;
Gott, KK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Gott, KK
;
Rea, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Rea, J
;
Yankaskas, JR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Yankaskas, JR
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
1997,
155
(05)
:1699
-1704
[3]
Heart-lung transplantation for patients under 10 with cystic fibrosis
[J].
BalfourLynn, IM
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
BalfourLynn, IM
;
Martin, I
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Martin, I
;
Whitehead, BF
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Whitehead, BF
;
Rees, PG
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Rees, PG
;
Elliott, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Elliott, MJ
;
deLeval, MR
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
deLeval, MR
.
ARCHIVES OF DISEASE IN CHILDHOOD,
1997,
76
(01)
:38
-40
[4]
Aerosol administration of a recombinant adenovirus expressing CFTR to cystic fibrosis patients: A phase I clinical trial
[J].
Bellon, G
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Bellon, G
;
MichelCalemard, L
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
MichelCalemard, L
;
Thouvenot, D
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Thouvenot, D
;
Jagneaux, V
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Jagneaux, V
;
Poitevin, F
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Poitevin, F
;
Malcus, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Malcus, C
;
Accart, N
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Accart, N
;
Layani, MP
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Layani, MP
;
Aymard, M
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Aymard, M
;
Bernon, H
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Bernon, H
;
Bienvenu, J
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Bienvenu, J
;
Courtney, M
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Courtney, M
;
Doring, G
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Doring, G
;
Gilly, B
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Gilly, B
;
Gilly, R
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Gilly, R
;
Lamy, D
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Lamy, D
;
Levrey, H
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Levrey, H
;
Morel, Y
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Morel, Y
;
Paulin, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Paulin, C
;
Perraud, F
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Perraud, F
;
Rodillon, L
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Rodillon, L
;
Sene, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Sene, C
;
So, S
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
So, S
;
TouraineMoulin, F
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
TouraineMoulin, F
;
Schatz, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Schatz, C
;
Pavirani, A
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Pavirani, A
.
HUMAN GENE THERAPY,
1997,
8
(01)
:15
-25
[5]
GENE-THERAPY FOR CYSTIC-FIBROSIS USING E1-DELETED ADENOVIRUS - A PHASE-I TRIAL IN THE NASAL CAVITY - THE UNIVERSITY-OF-NORTH-CAROLINA AT CHAPEL-HILL
[J].
BOUCHER, RC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
BOUCHER, RC
;
KNOWLES, MR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
KNOWLES, MR
;
JOHNSON, LG
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
JOHNSON, LG
;
OLSEN, JC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
OLSEN, JC
;
PICKLES, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
PICKLES, R
;
WILSON, JM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
WILSON, JM
;
ENGELHARDT, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
ENGELHARDT, J
;
YANG, YP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
YANG, YP
;
GROSSMAN, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
GROSSMAN, M
.
HUMAN GENE THERAPY,
1994,
5
(05)
:615
-639
[6]
Correcting temperature-sensitive protein folding defects
[J].
Brown, CR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
Brown, CR
;
HongBrown, LQ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
HongBrown, LQ
;
Welch, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
Welch, WJ
.
JOURNAL OF CLINICAL INVESTIGATION,
1997,
99
(06)
:1432
-1444
[7]
VARIABLE SEVERITY OF PULMONARY-DISEASE IN ADULTS WITH IDENTICAL CYSTIC-FIBROSIS MUTATIONS
[J].
BURKE, W
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
BURKE, W
;
AITKEN, ML
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
AITKEN, ML
;
CHEN, SH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
CHEN, SH
;
SCOTT, CR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
SCOTT, CR
.
CHEST,
1992,
102
(02)
:506
-509
[8]
DEFECTIVE INTRACELLULAR-TRANSPORT AND PROCESSING OF CFTR IS THE MOLECULAR-BASIS OF MOST CYSTIC-FIBROSIS
[J].
CHENG, SH
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
CHENG, SH
;
GREGORY, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
GREGORY, RJ
;
MARSHALL, J
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
MARSHALL, J
;
PAUL, S
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
PAUL, S
;
SOUZA, DW
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
SOUZA, DW
;
WHITE, GA
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
WHITE, GA
;
ORIORDAN, CR
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
ORIORDAN, CR
;
SMITH, AE
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
SMITH, AE
.
CELL,
1990,
63
(04)
:827
-834
[9]
FUNCTIONAL ACTIVATION OF THE CYSTIC-FIBROSIS TRAFFICKING MUTANT DELTA-F508-CFTR BY OVEREXPRESSION
[J].
CHENG, SH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
CHENG, SH
;
FANG, SL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
FANG, SL
;
ZABNER, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
ZABNER, J
;
MARSHALL, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
MARSHALL, J
;
PIRAINO, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
PIRAINO, S
;
SCHIAVI, SC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
SCHIAVI, SC
;
JEFFERSON, DM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
JEFFERSON, DM
;
WELSH, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
WELSH, MJ
;
SMITH, AE
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
SMITH, AE
.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY,
1995,
268
(04)
:L615
-L624
[10]
MUTATIONS IN THE CYSTIC-FIBROSIS GENE IN PATIENTS WITH CONGENITAL ABSENCE OF THE VAS-DEFERENS
[J].
CHILLON, M
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
CHILLON, M
;
CASALS, T
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
CASALS, T
;
MERCIER, B
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
MERCIER, B
;
BASSAS, L
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
BASSAS, L
;
LISSENS, W
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
LISSENS, W
;
SILBER, S
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
SILBER, S
;
ROMEY, MC
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
ROMEY, MC
;
RUIZROMERO, J
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
RUIZROMERO, J
;
VERLINGUE, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
VERLINGUE, C
;
CLAUSTRES, M
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
CLAUSTRES, M
;
NUNES, V
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
NUNES, V
;
FEREC, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
FEREC, C
;
ESTIVILL, X
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
ESTIVILL, X
.
NEW ENGLAND JOURNAL OF MEDICINE,
1995,
332
(22)
:1475
-1480
←
1
2
3
4
5
6
7
8
9
→
共 83 条
[1]
ALTON EWFW, 1990, EUR RESPIR J, V3, P922
[2]
The effects of panresistant bacteria in cystic fibrosis patients on lung transplant outcome
[J].
Aris, RM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Aris, RM
;
Gilligan, PH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Gilligan, PH
;
Neuringer, IP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Neuringer, IP
;
Gott, KK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Gott, KK
;
Rea, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Rea, J
;
Yankaskas, JR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV N CAROLINA,DEPT MICROBIOL IMMUNOL & PATHOL,CHAPEL HILL,NC 27599
Yankaskas, JR
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
1997,
155
(05)
:1699
-1704
[3]
Heart-lung transplantation for patients under 10 with cystic fibrosis
[J].
BalfourLynn, IM
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
BalfourLynn, IM
;
Martin, I
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Martin, I
;
Whitehead, BF
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Whitehead, BF
;
Rees, PG
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Rees, PG
;
Elliott, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
Elliott, MJ
;
deLeval, MR
论文数:
0
引用数:
0
h-index:
0
机构:
Transplant Unit, Gt. Ormond St. Hosp. Children NHS T., Great Ormond Street
deLeval, MR
.
ARCHIVES OF DISEASE IN CHILDHOOD,
1997,
76
(01)
:38
-40
[4]
Aerosol administration of a recombinant adenovirus expressing CFTR to cystic fibrosis patients: A phase I clinical trial
[J].
Bellon, G
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Bellon, G
;
MichelCalemard, L
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
MichelCalemard, L
;
Thouvenot, D
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Thouvenot, D
;
Jagneaux, V
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Jagneaux, V
;
Poitevin, F
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Poitevin, F
;
Malcus, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Malcus, C
;
Accart, N
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Accart, N
;
Layani, MP
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Layani, MP
;
Aymard, M
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Aymard, M
;
Bernon, H
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Bernon, H
;
Bienvenu, J
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Bienvenu, J
;
Courtney, M
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Courtney, M
;
Doring, G
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Doring, G
;
Gilly, B
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Gilly, B
;
Gilly, R
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Gilly, R
;
Lamy, D
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Lamy, D
;
Levrey, H
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Levrey, H
;
Morel, Y
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Morel, Y
;
Paulin, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Paulin, C
;
Perraud, F
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Perraud, F
;
Rodillon, L
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Rodillon, L
;
Sene, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Sene, C
;
So, S
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
So, S
;
TouraineMoulin, F
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
TouraineMoulin, F
;
Schatz, C
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Schatz, C
;
Pavirani, A
论文数:
0
引用数:
0
h-index:
0
机构:
TRANSGENE SA, F-67082 STRASBOURG, FRANCE
Pavirani, A
.
HUMAN GENE THERAPY,
1997,
8
(01)
:15
-25
[5]
GENE-THERAPY FOR CYSTIC-FIBROSIS USING E1-DELETED ADENOVIRUS - A PHASE-I TRIAL IN THE NASAL CAVITY - THE UNIVERSITY-OF-NORTH-CAROLINA AT CHAPEL-HILL
[J].
BOUCHER, RC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
BOUCHER, RC
;
KNOWLES, MR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
KNOWLES, MR
;
JOHNSON, LG
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
JOHNSON, LG
;
OLSEN, JC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
OLSEN, JC
;
PICKLES, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
PICKLES, R
;
WILSON, JM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
WILSON, JM
;
ENGELHARDT, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
ENGELHARDT, J
;
YANG, YP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
YANG, YP
;
GROSSMAN, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, PHILADELPHIA, PA 19104 USA
UNIV PENN, PHILADELPHIA, PA 19104 USA
GROSSMAN, M
.
HUMAN GENE THERAPY,
1994,
5
(05)
:615
-639
[6]
Correcting temperature-sensitive protein folding defects
[J].
Brown, CR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
Brown, CR
;
HongBrown, LQ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
HongBrown, LQ
;
Welch, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
UNIV CALIF SAN FRANCISCO,DEPT PHYSIOL,SAN FRANCISCO,CA 94143
Welch, WJ
.
JOURNAL OF CLINICAL INVESTIGATION,
1997,
99
(06)
:1432
-1444
[7]
VARIABLE SEVERITY OF PULMONARY-DISEASE IN ADULTS WITH IDENTICAL CYSTIC-FIBROSIS MUTATIONS
[J].
BURKE, W
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
BURKE, W
;
AITKEN, ML
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
AITKEN, ML
;
CHEN, SH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
CHEN, SH
;
SCOTT, CR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
SCOTT, CR
.
CHEST,
1992,
102
(02)
:506
-509
[8]
DEFECTIVE INTRACELLULAR-TRANSPORT AND PROCESSING OF CFTR IS THE MOLECULAR-BASIS OF MOST CYSTIC-FIBROSIS
[J].
CHENG, SH
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
CHENG, SH
;
GREGORY, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
GREGORY, RJ
;
MARSHALL, J
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
MARSHALL, J
;
PAUL, S
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
PAUL, S
;
SOUZA, DW
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
SOUZA, DW
;
WHITE, GA
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
WHITE, GA
;
ORIORDAN, CR
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
ORIORDAN, CR
;
SMITH, AE
论文数:
0
引用数:
0
h-index:
0
机构:
Genzyme Corporation, Framingham
SMITH, AE
.
CELL,
1990,
63
(04)
:827
-834
[9]
FUNCTIONAL ACTIVATION OF THE CYSTIC-FIBROSIS TRAFFICKING MUTANT DELTA-F508-CFTR BY OVEREXPRESSION
[J].
CHENG, SH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
CHENG, SH
;
FANG, SL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
FANG, SL
;
ZABNER, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
ZABNER, J
;
MARSHALL, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
MARSHALL, J
;
PIRAINO, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
PIRAINO, S
;
SCHIAVI, SC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
SCHIAVI, SC
;
JEFFERSON, DM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
JEFFERSON, DM
;
WELSH, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
WELSH, MJ
;
SMITH, AE
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV IOWA, COLL MED, DEPT INTERNAL MED & PHYSIOL & BIOPHYS, IOWA CITY, IA 52242 USA
SMITH, AE
.
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY,
1995,
268
(04)
:L615
-L624
[10]
MUTATIONS IN THE CYSTIC-FIBROSIS GENE IN PATIENTS WITH CONGENITAL ABSENCE OF THE VAS-DEFERENS
[J].
CHILLON, M
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
CHILLON, M
;
CASALS, T
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
CASALS, T
;
MERCIER, B
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
MERCIER, B
;
BASSAS, L
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
BASSAS, L
;
LISSENS, W
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
LISSENS, W
;
SILBER, S
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
SILBER, S
;
ROMEY, MC
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
ROMEY, MC
;
RUIZROMERO, J
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
RUIZROMERO, J
;
VERLINGUE, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
VERLINGUE, C
;
CLAUSTRES, M
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
CLAUSTRES, M
;
NUNES, V
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
NUNES, V
;
FEREC, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
FEREC, C
;
ESTIVILL, X
论文数:
0
引用数:
0
h-index:
0
机构:
HOSP DURAN & REYNALS, CANC RES INST, DEPT MOLEC GENET, E-08907 LHOSPITALET DE LLOBREGAT, SPAIN
ESTIVILL, X
.
NEW ENGLAND JOURNAL OF MEDICINE,
1995,
332
(22)
:1475
-1480
←
1
2
3
4
5
6
7
8
9
→