Alveolar capillary dysplasia, with and without misalignment of pulmonary veins: An association of congenital anomalies

被引:37
作者
Garola, RE [1 ]
Thibeault, DW [1 ]
机构
[1] Univ Missouri, Childrens Mercy Hosp, Dept Pathol, Sch Med, Kansas City, MO 64108 USA
关键词
alveolar capillary dysplasia; malformations;
D O I
10.1055/s-2007-993907
中图分类号
R71 [妇产科学];
学科分类号
100211 ;
摘要
Two new cases of alveolar capillary dysplasia (ACD), one without misalignment of the pulmonary vessels (MLV), are reported. They are unique for their association with complex cardiac malformations and asplenia. By reporting these cases we want to stress that ACD is associated with multiple malformations, and that the absence of MLV does not rule out the diagnosis of ACD.
引用
收藏
页码:103 / 107
页数:5
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