The Obstructed Hemivagina, Ipsilateral Renal Anomaly, and Uterine Didelphys Triad and the Subsequent Manifestation of Cervical Aplasia

被引:18
作者
Sabdia, S. [1 ]
Sutton, B. [2 ]
Kimble, R. M. N. [1 ,3 ]
机构
[1] Royal Brisbane & Womens Hosp, Dept Obstet & Gynaecol, Queensland Statewide Paediat & Adolescent Gynaeco, Herston, Qld 4029, Australia
[2] Royal Brisbane & Womens Hosp, Dept Med Imaging, Herston, Qld 4029, Australia
[3] Univ Queensland, Sch Med, Brisbane, Qld, Australia
关键词
Obstructed hemivagina; Uterine didelphys; Absent kidney; Cervical aplasia; 16p11.2; UTERUS DIDELPHYS; AGENESIS; ATRESIA; DIAGNOSIS; DELETION;
D O I
10.1016/j.jpag.2014.02.001
中图分类号
R71 [妇产科学];
学科分类号
100211 [妇产科学];
摘要
Study Objective: To compare a case series of the obstructed hemivagina, ipsilateral renal anomaly and uterine didelphys triad with the literature, with a focus on a subset of patients with cervical aplasia. Design, Setting, and Participants: A retrospective case series was conducted of all patients with the triad managed between 2005-2013 at a tertiary center for adolescent gynecology. Results: Similarities in this cohort, compared to the literature, included heterogeneity of presentation, presence of endometriosis, and asymmetry of affected side. Notable differences included 1 patient with a 16p11.2 microdeletion and 2 patients with subsequent unilateral cervical aplasia. All patients underwent magnetic resonance imaging for diagnosis. Vaginal septum division was performed in 8 cases and excision in 1 case. Both cases with cervical aplasia ultimately underwent hemi-hysterectomy, and highlight the implications of this rare variant in regards to its existence, limitations of magnetic resonance imaging in this context, and suggestions for improvement in diagnosis and management. Conclusion: The complexity of these cases, especially the evolving manifestation of cervical aplasia postoperatively, illustrates the need to recognize limitations in imaging and divergence in definitive management.
引用
收藏
页码:375 / 378
页数:4
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