Long QT syndrome manifested as fetal ventricular tachycardia and intermittent AV block

被引:6
作者
Lin, MT [1 ]
Wu, MH [1 ]
Hsieh, FJ [1 ]
Wang, JK [1 ]
Teng, RJ [1 ]
Tsou, KIY [1 ]
Lue, HC [1 ]
机构
[1] Natl Taiwan Univ Hosp, Dept Pediat, Taipei 10016, Taiwan
关键词
long QT; ventricular tachycardia; prenatal diagnosis; sonography;
D O I
10.1055/s-2007-993915
中图分类号
R71 [妇产科学];
学科分类号
100211 ;
摘要
A case of long QT syndrome diagnosed in the early neonatal period is described. This full-term female baby had intermittent atrioventricular (AV) block and ventricular tachycardia detected antenatally at the gestational age of 26 weeks. Sinus rhythm with prolonged QT interval (QTc = 0.636 sec) was found soon after birth. She developed variable degree of AV block with alternating left and right bundle branch block, which suggested the presence of multilevel AV block. Her mother had no lupus autoantibodies. Auditory brain stem evoked potential was normal. Family study revealed QT prolongation in her grandmother. Her condition improved after pacemaker implantation and oral beta-blocker usage.
引用
收藏
页码:145 / 147
页数:3
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