Susac's syndrome: a rare cause of fluctuating sensorineural hearing loss

被引:28
作者
Bateman, ND [1 ]
Johnson, IJM [1 ]
Gibbin, KP [1 ]
机构
[1] Univ Nottingham Hosp, Queens Med Ctr, Dept Otolaryngol Head & Neck Surg, Nottingham NG7 2UH, England
关键词
hearing loss; sensorineural;
D O I
10.1017/S0022215100139374
中图分类号
R76 [耳鼻咽喉科学];
学科分类号
100213 ;
摘要
Susac's syndrome is extremely rare and is characterized by the clinical triad of encephalopathy, retinal artery occlusion and deafness. A case of this rare syndrome is presented and for the first time the fluctuating nature of the hearing loss is demonstrated. The site and nature of the hearing loss has been investigated. The value of neural hearing loss as a method of monitoring the clinical severity is discussed.
引用
收藏
页码:1072 / 1074
页数:3
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