The Wiskott-Aldrich syndrome

被引:26
作者
Ochs, HD [1 ]
机构
[1] Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
来源
SPRINGER SEMINARS IN IMMUNOPATHOLOGY | 1998年 / 19卷 / 04期
关键词
D O I
10.1007/BF00792601
中图分类号
R392 [医学免疫学]; Q939.91 [免疫学];
学科分类号
100102 ;
摘要
[No abstract available]
引用
收藏
页码:435 / 458
页数:24
相关论文
共 108 条
[1]  
ALDRICH RA, 1954, PEDIATRICS, V13, P133
[2]   NONSPECIFIC HELPER EFFECT OF MIXED LYMPHOCYTE REACTIONS ON INDUCTION OF T-CELL-MEDIATED IMMUNITY INVITRO [J].
ALTMAN, A ;
COHEN, IR .
EUROPEAN JOURNAL OF IMMUNOLOGY, 1974, 4 (08) :577-580
[3]   ATTENUATED FORM OF WISKOTT-ALDRICH SYNDROME [J].
ALVAREZA.C ;
DORANTES, S ;
TORO, AH ;
BELLO, A ;
CUELLAR, J .
JOURNAL OF PEDIATRICS, 1973, 82 (01) :175-176
[4]  
AMIET A, 1963, ANN PAEDIATR-BASEL, V201, P315
[5]   Two GTPases, cdc42 and rac, bind directly to a protein implicated in the immunodeficiency disorder Wiskott-Aldrich syndrome [J].
Aspenstrom, P ;
Lindberg, U ;
Hall, A .
CURRENT BIOLOGY, 1996, 6 (01) :70-75
[6]  
AYOUB EM, 1968, J LAB CLIN MED, V72, P971
[7]   NATURE OF PLATELET DEFECT IN WISKOTT-ALDRICH SYNDROME [J].
BALDINI, MG .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1972, 201 (OCT27) :437-&
[8]   Wiskott-Aldrich syndrome protein (WASp) is a binding partner for c-Src family protein-tyrosine kinases [J].
Banin, S ;
Truong, O ;
Katz, DR ;
Waterfield, MD ;
Brickell, PM ;
Gout, I .
CURRENT BIOLOGY, 1996, 6 (08) :981-988
[9]  
BASILE GD, 1989, LANCET, V2, P1319
[10]   Isolated X-linked thrombocytopenia in two unrelated families is associated with point mutations in the Wiskott-Aldrich syndrome protein gene [J].
Basile, GD ;
Lagelouse, RD ;
Lambert, N ;
Schwarz, K ;
leMareck, B ;
Odent, S ;
Schlegel, N ;
Fischer, A .
JOURNAL OF PEDIATRICS, 1996, 129 (01) :56-62