Cognitive functioning in adults with Williams syndrome

被引:124
作者
Howlin, P
Davies, M
Udwin, O
机构
[1] St George Hosp, Sch Med, Dept Psychol, London SW17 0RE, England
[2] Queens Univ Belfast, Belfast, Antrim, North Ireland
[3] Mary Sheridan Child Hlth, Lambeth Healthcare NHS Trust, London, England
关键词
adulthood; educational attainment; intelligence; natural history; Williams syndrome;
D O I
10.1111/1469-7610.00312
中图分类号
B844 [发展心理学(人类心理学)];
学科分类号
040202 ;
摘要
This paper reports the results of cognitive, linguistic, and academic assessments in a representative sample of 62 adults with Williams syndrome. The average age of the group was 26 years and their mean full scale IQ was 61. Differences between Verbal and Performance IQ, and between receptive and expressive language skills, were smaller than generally found in studies of children with this condition. However, an examination of subtest scores revealed an almost identical cognitive profile to that found in children. Skills in other areas, such as reading, spelling, arithmetic, and social adaptation remained at a low level, with functioning generally being around a 6-8-year age equivalent. The consistency of reports on intellectual abilities in both child and adult studies of individuals with Williams syndrome lends increased support to the notion of a syndrome specific pattern of cognitive, linguistic, and adaptive functioning.
引用
收藏
页码:183 / 189
页数:7
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