Ocular tumoral calcinosis - A clinicopathologic study

被引:23
作者
Ghanchi, F [1 ]
Ramsay, A [1 ]
Coupland, S [1 ]
Barr, D [1 ]
Lee, WR [1 ]
机构
[1] WESTERN INFIRM & ASSOCIATED HOSP,DEPT PATHOL,GLASGOW G11 6NT,LANARK,SCOTLAND
关键词
D O I
10.1001/archopht.1996.01100130337022
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
Tumoral calcinosis is a rare systemic disorder characterized by para-articular ectopic soft-tissue calcification. This case report describes the ophthalmic features (palpebral conjunctival calcific nodules, the white limbal girdle of Vogt, disc drusen, and angioid streaks) in a 38-year-old Asian woman who had tumoral calcinosis associated with hyperphosphatemia. A morphologic study of the calcified nodules on the palpebral conjunctiva disclosed deposition of hydroxyapatite crystals in an extracellular matrix (deposit) containing alcianophilic mucopolysaccharides. Excision of the eyelid nodules was not followed by recurrence.
引用
收藏
页码:341 / 345
页数:5
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