Persistent Mullerian duct syndrome

被引:7
作者
Rizk, DEE
Ezimokhai, M
Hussein, AS
Gerami, S
Deb, P
机构
[1] Fac Med & Hlth Sci, Dept Obstet & Gynecol, Al Ain, U Arab Emirates
[2] United Arab Emirates Univ, Dept Paediat Surg, Al Ain, U Arab Emirates
[3] Al Ain Hosp, Dept Obstet & Gynecol, Al Ain, U Arab Emirates
关键词
cryptorchidism; inguinal hernia; persistent Mullerian duct syndrome; undescended testis; uterine hernia syndrome;
D O I
10.1007/s004040050208
中图分类号
R71 [妇产科学];
学科分类号
100211 ;
摘要
We report an 18-month old male presenting with a right-sided inguinal hernia and undescended testes. At herniotomy, a uterus and two fallopian tubes were found in the pelvic peritoneum adjacent to the two gonads which received their blood supply partly along the Mullerian duct remnants. The gonads were testes by histological examination. Bilateral orchiopexy was performed without removal of the Mullerian structures for fear of jeopardizing the testicular blood supply. The diagnosis of persistent Mullerian duct syndrome was confirmed postoperatively by genetic and hormonal investigations.
引用
收藏
页码:105 / 107
页数:3
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