Dramatic effect of sirolimus on renal angiomyolipomas in a patient with tuberous sclerosis complex

被引：61

作者：

Herry, Isabelle

Neukirch, Catherine

Debray, Marie-Pierre

Mignon, Francoise

Crestani, Bruno

机构：

[1] Hop Bichat Claude Bernard, AP HP, Serv Pneumol, F-75877 Paris 18, France

[2] Univ Paris 07, F-75221 Paris, France

[3] Hop Bichat Claude Bernard, AP HP, Serv Radiol, F-75877 Paris 18, France

[4] Hop Bichat Claude Bernard, AP HP, Serv Nephrol, F-75877 Paris 18, France

来源：

EUROPEAN JOURNAL OF INTERNAL MEDICINE | 2007年 / 18卷 / 01期

关键词：

angiomyolipomas; tuberous sclerosis complex; lymphangioleiomyomatosis; sirolimus;

D O I：

10.1016/j.ejim.2006.07.017

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Angiomyolipomas are very common in patients with tuberous sclerosis complex (TSC) and cause substantial morbidity. Until now, arterial embolization has been the recommended treatment for symptomatic patients. We report the case of a woman with TSC and giant angiolipomas in whom sirolimus induced a dramatic reduction in bilateral renal tumors. (C) 2006 European Federation of Internal Medicine. Published by Elsevier B.V. All rights reserved.

引用

页码：76 / 77

页数：2

共 6 条

[1] PULMONARY TUBEROUS SCLEROSIS [J].