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Inborn errors of metabolism:: cause of oxidative stress?
被引:29
作者
:
Colomé, C
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Serv Bioquim, Barcelona 08950, Spain
Colomé, C
Sierra, C
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Serv Bioquim, Barcelona 08950, Spain
Sierra, C
Vilaseca, A
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Serv Bioquim, Barcelona 08950, Spain
Vilaseca, A
机构
:
[1]
Univ Barcelona, Hosp St Joan Deu, Serv Bioquim, Barcelona 08950, Spain
[2]
Univ Barcelona, Hosp St Joan Deu, Lab Invest, Barcelona 08950, Spain
来源
:
MEDICINA CLINICA
|
2000年
/ 115卷
/ 03期
关键词
:
D O I
:
10.1016/S0025-7753(00)71479-5
中图分类号
:
R5 [内科学];
学科分类号
:
1002
[临床医学]
;
100201
[内科学]
;
摘要
:
引用
收藏
页码:111 / 117
页数:7
相关论文
共 57 条
[1]
Artuch R, 1999, AM J CLIN NUTR, V70, P892
[2]
Ubiquinone:: Metabolism and functions.: Ubiquinone deficiency and its implication in mitochondrial encephalomyopathies.: Treatment with ubiquinone
[J].
Artuch, R
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Artuch, R
;
Colomé, C
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Colomé, C
;
Vilaseca, A
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Vilaseca, A
;
Pineda, M
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Pineda, M
;
Campistol, J
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Campistol, J
.
REVISTA DE NEUROLOGIA,
1999,
29
(01)
:59
-63
[3]
Biochemical monitoring of the treatment in paediatric patients with mitochondrial disease
[J].
Artuch, R
论文数:
0
引用数:
0
h-index:
0
机构:
Hosp Univ Sant Joan de Deu, Serv Bioquim, Barcelona 08950, Spain
Artuch, R
;
Vilaseca, MA
论文数:
0
引用数:
0
h-index:
0
机构:
Hosp Univ Sant Joan de Deu, Serv Bioquim, Barcelona 08950, Spain
Vilaseca, MA
;
Pineda, M
论文数:
0
引用数:
0
h-index:
0
机构:
Hosp Univ Sant Joan de Deu, Serv Bioquim, Barcelona 08950, Spain
Pineda, M
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1998,
21
(08)
:837
-845
[4]
Mitochondria, free radicals, and neurodegeneration
[J].
Beal, MF
论文数:
0
引用数:
0
h-index:
0
机构:
HARVARD UNIV, SCH MED, BOSTON, MA 02114 USA
HARVARD UNIV, SCH MED, BOSTON, MA 02114 USA
Beal, MF
.
CURRENT OPINION IN NEUROBIOLOGY,
1996,
6
(05)
:661
-666
[5]
SEQUENTIAL DAMAGE IN MITOCHONDRIAL COMPLEXES BY PEROXIDATIVE STRESS
[J].
BENZI, G
论文数:
0
引用数:
0
h-index:
0
机构:
Institute of Pharmacology, Faculty of Sciences, University of Pavia, Pavia, 27100
BENZI, G
;
论文数:
引用数:
h-index:
机构:
CURTI, D
;
论文数:
引用数:
h-index:
机构:
PASTORIS, O
;
MARZATICO, F
论文数:
0
引用数:
0
h-index:
0
机构:
Institute of Pharmacology, Faculty of Sciences, University of Pavia, Pavia, 27100
MARZATICO, F
;
论文数:
引用数:
h-index:
机构:
VILLA, RF
;
DAGANI, F
论文数:
0
引用数:
0
h-index:
0
机构:
Institute of Pharmacology, Faculty of Sciences, University of Pavia, Pavia, 27100
DAGANI, F
.
NEUROCHEMICAL RESEARCH,
1991,
16
(12)
:1295
-1302
[6]
PLASMA ANTIOXIDANT CAPACITY IN 2 CASES OF TYROSINEMIA TYPE-1 - ONE CASE TREATED WITH NTBC
[J].
BIRD, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
BIRD, S
;
MILLER, NJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
MILLER, NJ
;
COLLINS, JE
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
COLLINS, JE
;
RICEEVANS, CA
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
RICEEVANS, CA
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1995,
18
(02)
:123
-126
[7]
Oxidative DNA damage processing in nuclear and mitochondrial DNA
[J].
Bohr, VA
论文数:
0
引用数:
0
h-index:
0
机构:
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
Bohr, VA
;
Dianov, GL
论文数:
0
引用数:
0
h-index:
0
机构:
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
Dianov, GL
.
BIOCHIMIE,
1999,
81
(1-2)
:155
-160
[8]
BOLANOS JP, 1995, J NEUROCHEM, V64, P1965
[9]
CURRENT RESEARCH IN THE ORGANIC ACIDURIAS
[J].
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
CHALMERS, RA
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1989,
12
(02)
:225
-239
[10]
HYDROPEROXIDE METABOLISM IN MAMMALIAN ORGANS
[J].
CHANCE, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH, INST PHYS CHEM, D-8000 MUNICH 2, GERMANY
CHANCE, B
;
SIES, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH, INST PHYS CHEM, D-8000 MUNICH 2, GERMANY
SIES, H
;
BOVERIS, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH, INST PHYS CHEM, D-8000 MUNICH 2, GERMANY
BOVERIS, A
.
PHYSIOLOGICAL REVIEWS,
1979,
59
(03)
:527
-605
←
1
2
3
4
5
6
→
共 57 条
[1]
Artuch R, 1999, AM J CLIN NUTR, V70, P892
[2]
Ubiquinone:: Metabolism and functions.: Ubiquinone deficiency and its implication in mitochondrial encephalomyopathies.: Treatment with ubiquinone
[J].
Artuch, R
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Artuch, R
;
Colomé, C
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Colomé, C
;
Vilaseca, A
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Vilaseca, A
;
Pineda, M
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Pineda, M
;
Campistol, J
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Barcelona, Hosp St Joan Deu, Unitat Integrada, Hosp Clin,Serv Bioquim, E-08950 Barcelona, Spain
Campistol, J
.
REVISTA DE NEUROLOGIA,
1999,
29
(01)
:59
-63
[3]
Biochemical monitoring of the treatment in paediatric patients with mitochondrial disease
[J].
Artuch, R
论文数:
0
引用数:
0
h-index:
0
机构:
Hosp Univ Sant Joan de Deu, Serv Bioquim, Barcelona 08950, Spain
Artuch, R
;
Vilaseca, MA
论文数:
0
引用数:
0
h-index:
0
机构:
Hosp Univ Sant Joan de Deu, Serv Bioquim, Barcelona 08950, Spain
Vilaseca, MA
;
Pineda, M
论文数:
0
引用数:
0
h-index:
0
机构:
Hosp Univ Sant Joan de Deu, Serv Bioquim, Barcelona 08950, Spain
Pineda, M
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1998,
21
(08)
:837
-845
[4]
Mitochondria, free radicals, and neurodegeneration
[J].
Beal, MF
论文数:
0
引用数:
0
h-index:
0
机构:
HARVARD UNIV, SCH MED, BOSTON, MA 02114 USA
HARVARD UNIV, SCH MED, BOSTON, MA 02114 USA
Beal, MF
.
CURRENT OPINION IN NEUROBIOLOGY,
1996,
6
(05)
:661
-666
[5]
SEQUENTIAL DAMAGE IN MITOCHONDRIAL COMPLEXES BY PEROXIDATIVE STRESS
[J].
BENZI, G
论文数:
0
引用数:
0
h-index:
0
机构:
Institute of Pharmacology, Faculty of Sciences, University of Pavia, Pavia, 27100
BENZI, G
;
论文数:
引用数:
h-index:
机构:
CURTI, D
;
论文数:
引用数:
h-index:
机构:
PASTORIS, O
;
MARZATICO, F
论文数:
0
引用数:
0
h-index:
0
机构:
Institute of Pharmacology, Faculty of Sciences, University of Pavia, Pavia, 27100
MARZATICO, F
;
论文数:
引用数:
h-index:
机构:
VILLA, RF
;
DAGANI, F
论文数:
0
引用数:
0
h-index:
0
机构:
Institute of Pharmacology, Faculty of Sciences, University of Pavia, Pavia, 27100
DAGANI, F
.
NEUROCHEMICAL RESEARCH,
1991,
16
(12)
:1295
-1302
[6]
PLASMA ANTIOXIDANT CAPACITY IN 2 CASES OF TYROSINEMIA TYPE-1 - ONE CASE TREATED WITH NTBC
[J].
BIRD, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
BIRD, S
;
MILLER, NJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
MILLER, NJ
;
COLLINS, JE
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
COLLINS, JE
;
RICEEVANS, CA
论文数:
0
引用数:
0
h-index:
0
机构:
UNITED MED & DENT SCH,DIV BIOCHEM,FREE RAD RES GRP,LONDON,ENGLAND
RICEEVANS, CA
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1995,
18
(02)
:123
-126
[7]
Oxidative DNA damage processing in nuclear and mitochondrial DNA
[J].
Bohr, VA
论文数:
0
引用数:
0
h-index:
0
机构:
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
Bohr, VA
;
Dianov, GL
论文数:
0
引用数:
0
h-index:
0
机构:
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
NIA, Genet Mol Lab, NIH, Baltimore, MD 21224 USA
Dianov, GL
.
BIOCHIMIE,
1999,
81
(1-2)
:155
-160
[8]
BOLANOS JP, 1995, J NEUROCHEM, V64, P1965
[9]
CURRENT RESEARCH IN THE ORGANIC ACIDURIAS
[J].
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
CHALMERS, RA
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1989,
12
(02)
:225
-239
[10]
HYDROPEROXIDE METABOLISM IN MAMMALIAN ORGANS
[J].
CHANCE, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH, INST PHYS CHEM, D-8000 MUNICH 2, GERMANY
CHANCE, B
;
SIES, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH, INST PHYS CHEM, D-8000 MUNICH 2, GERMANY
SIES, H
;
BOVERIS, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH, INST PHYS CHEM, D-8000 MUNICH 2, GERMANY
BOVERIS, A
.
PHYSIOLOGICAL REVIEWS,
1979,
59
(03)
:527
-605
←
1
2
3
4
5
6
→