Inhibitory effect of 3-hydroxyacyl-CoAs and other long-chain fatty acid beta-oxidation intermediates on mitochondrial oxidative phosphorylation

被引：39

作者：

Ventura, FV ^{[1
]}

Ruiter, JPN ^{[1
]}

Ijlst, L ^{[1
]}

deAlmeida, IT ^{[1
]}

Wanders, RJA ^{[1
]}

机构：

[1] UNIV LISBON,FAC FAMACA,CTR METAB & GENET,P-1699 LISBON,PORTUGAL

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1996年 / 19卷 / 02期

关键词：

D O I：

10.1007/BF01799419

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：161 / 164

页数：4

共 7 条

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[5] PEROXISOMAL FATTY-ACID BETA-OXIDATION IN RELATION TO THE ACCUMULATION OF VERY LONG-CHAIN FATTY-ACIDS IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH ZELLWEGER SYNDROME AND OTHER PEROXISOMAL DISORDERS [J].

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[6] STUDIES ON MITOCHONDRIAL OXIDATIVE-PHOSPHORYLATION IN PERMEABILIZED HUMAN SKIN FIBROBLASTS - APPLICATION TO MITOCHONDRIAL ENCEPHALOMYOPATHIES [J].

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