The first case of new variant Creutzfeldt-Jakob disease in France: Clinical data and neuropathological findings

被引：10

作者：

Streichenberger N. ^{[1
,2
]}

Jordan D. ^{[1
,2
]}

Verejan I. ^{[1
,2
]}

Souchier C.

Philippeau F. ^{[1
,2
]}

Gros E. ^{[1
,2
]}

Mottolese C. ^{[2
]}

Ostrowsky K. ^{[2
]}

Perret-Liaudet A. ^{[2
]}

Laplanche J.L. ^{[3
]}

Hermier M. ^{[2
]}

Deslys J.P.

Chazot G. ^{[2
]}

Kopp N. ^{[1
,2
]}

机构：

[1] Lab. des Maladies à Prions, Department of Neuropathology, Hôpital Neurologique, 69003 Lyon

[2] Hôpital Neurologique, 69003 Lyon

[3] Hôpital Lariboisière, Paris

来源：

Acta Neuropathologica | 2000年 / 99卷 / 6期

关键词：

Creutzfeldt-jakob disease; Neuropathology; New variant;

D O I：

10.1007/s004010051184

中图分类号：

学科分类号：

摘要：

Clinical data and autopsy findings in a case of new variant Creutzfeldt-Jakob disease (vCJD) are reported. this case, the first histologically confirmed case described outside the United Kingdom, very much resembles the cases described by WiIl et al. Neuropathological studies failed to reveal any conspicuous clues that could be relevant for understanding the pathophysiology of the disease. For epidemiological surveillance, neuropathologists should scrutinize suspected cases keeping in mind the possibility of vCJD.

引用

页码：704 / 708

页数：4

共 10 条

[1]

Aguzzi A., Blattler T., Klein M., Raber A., Weissmann C., Brandner S., Telencephalic brain grafts in the study of scrapie pathogenesis, Transmissible Subacute Encephalopathies, pp. 173-184, (1996)

[2]

Chazot G., Broussolle E., Lapras C., Blattler T., Aguzzi A., Kopp N., New variant of Creutzfeld-Jakob disease in a 26-year-old french man, Lancet, 347, (1996)

[3]

Deslys J.P., Lasmezas C., Streichenberger N., Hill A., Collinge J., Dormont D., Kopp N., New variant Creutzfeld-Jakob disease in France, Lancet, 349, pp. 30-31, (1997)

[4]

Ironside J.W., The new variant form of Creutzfeld-Jakob disease: A novel prion protein amyloid disorder, Int J Clin Invest, 4, pp. 66-69, (1997)

[5]

Ironside J.W., Bell J.E., Pathology of prion diseases, Prion Diseases, pp. 57-88, (1997)

[6]

Kopp N., Streichenberger N., Deslys J.P., Laplanche J.L., Chazot G., Creutzfeldt-Jakob disease in a 52-year-old woman with florid plaques, Lancet, 348, pp. 1239-1240, (1996)

[7]

Wells G.A.H., Wilesmith J.W., McGill I.S., Bovine spongiform encephalopathy, Brain Pathol, 1, pp. 65-78, (1991)

[8]

Will R.G., Ironside J., Zeidler M., Cousens S.N., Estibeiro K., Alperovitch A., Poser S., Pocchiari M., Hofman A., Smith P.G., A new variant of Creutzfeldt-Jakob disease in the UK, Lancet, 347, pp. 921-925, (1996)

[9]

Zeidler M., Stewart G.E., Barraclough C.R., Bateman D.E., Bates D., Burn D.J., Colchester A.C., Durward W., Fletcher N.A., Hawkins S.A., Mackenzie J.M., Will R.G., New variant Creutzfeldt-Jakob disease: Neurological features and diagnostics test, Lancet, 350, pp. 903-908, (1997)

[10]

Zeidler M., Johnstone E.C., Bamber R.W.K., Dickens C.M., Fisher C.J., Francis A.F., Goldbeck R., Higgo R., Johnson-Sabine E.C., Lodge G.J., McGarry P., Mitchell S., Tarlo L., Ryley P., Will R.G., New variant Creutzfeldt-Jakob disease: Psychiatric features, Lancet, 350, pp. 908-910, (1997)

← 1 →