Congenital complete heart block: Fetal management protocol, review of the literature, and report of the smallest succesful pacemaker implantation

被引：36

作者：

Donofrio M.T. ^{[1
]}

Gullquist S.D. ^{[1
]}

Mehta I.D. ^{[2
]}

Moskowitz W.B. ^{[1
]}

机构：

[1] Department of Pediatrics, Medical College of Virginia, Hosp. of Virginia Commonwealth Univ., Richmond, VA 23298

[2] Department of Surgery, Medical College of Virginia, Hosp. of Virginia Commonwealth Univ., Richmond, VA 23298

来源：

Journal of Perinatology | 2004年 / 24卷 / 2期

关键词：

D O I：

10.1038/sj.jp.7211038

中图分类号：

学科分类号：

摘要：

Fetuses with complete heart block have an increased mortality with most deaths occurring in utero or during infancy. The cardiac evaluation of these fetuses is difficult since the ventriclular rate is low and the heart is dilated. We have implemented a strategy that includes the biophysical profile, which assesses fetal well-being, in combination with the cardiovascular profile that assesses cardiac function and the circulation. We present two cases of fetal complete heart block in which early delivery was recommended due to worsening cardiovascular profile scores. Biophysical profile scores were normal. Both babies were successfully treated, despite having risk factors that predicted poor outcomes. We hypothesize that our management protocol initiated intervention before fetal compromise, hydrops, and myocardial damage occurred. We recommend an evaluation of heart function in addition to an assessment of feral well-being in fetuses with complete heart block. Early should be considered if there is evidence of distress and/or deteriorating cardiac function. © Nature Publishing Group All rights reserved.

引用

页码：112 / 117

页数：5

共 11 条

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