STAPHYLOCOCCAL SCALDED SKIN SYNDROME (SSSS) AND CONSECUTIVE SEPTICEMIA IN A PRETERM INFANT

被引:17
作者
HOFFMANN, R [1 ]
LOHNER, M [1 ]
BOHM, N [1 ]
SCHAEFER, HE [1 ]
LEITITIS, J [1 ]
机构
[1] UNIV FREIBURG, FAC PAEDIAT MED, W-7800 FREIBURG, GERMANY
关键词
SSSS; EXANTHEMATIC NECROLYSIS; ULTRASTRUCTURE; DESMOSOMES;
D O I
10.1016/S0344-0338(11)80499-1
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Staphylococcal scaled-skin syndrome (SSSS) is a toxin-related epidermolytic disease that usually affects infants and children under 5 years. We report herein a case of a premature infant who had developed SSSS after an infection of the pharynx with staphylococci and who died of septicaemia due to pseudomonas aeruginosa. The primary mechanism of action of epidermolysin still remains unknown. We demonstrate that acantholysis is due to an early edema of the intercellular space with separation of ultrastructurally unaltered desmosomes.
引用
收藏
页码:77 / 81
页数:5
相关论文
共 14 条
[1]  
BALDA BR, 1982, MUNCHEN MED WOCHEN, V124, P739
[2]   STAPHYLOCOCCAL TOXIC EPIDERMAL NECROLYSIS - PATHOGENESIS AND STUDIES ON SUBCELLULAR SITE OF ACTION OF EXFOLIATIN [J].
ELIAS, PM ;
FRITSCH, P ;
DAHL, MV ;
WOLFF, K .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1975, 65 (06) :501-512
[3]   STAPHYLOCOCCAL SCALDED SKIN SYNDROME [J].
ELIAS, PM ;
FRITSCH, P ;
EPSTEIN, EH .
ARCHIVES OF DERMATOLOGY, 1977, 113 (02) :207-219
[4]   FATE OF STAPHYLOCOCCAL EXFOLIATIN IN NEWBORN AND ADULT MICE [J].
FRITSCH, P ;
ELIAS, P ;
VARGA, J .
BRITISH JOURNAL OF DERMATOLOGY, 1976, 95 (03) :275-284
[5]  
LILLIBRIDGE CB, 1972, PEDIATRICS, V50, P728
[7]   REQUIEM FOR TOXIC EPIDERMAL NECROLYSIS [J].
LYELL, A .
BRITISH JOURNAL OF DERMATOLOGY, 1990, 122 (06) :837-838
[8]   TOXIC EPIDERMAL NECROLYSIS (THE SCALDED SKIN SYNDROME) - REAPPRAISAL [J].
LYELL, A .
BRITISH JOURNAL OF DERMATOLOGY, 1979, 100 (01) :69-+
[9]   A REVIEW OF TOXIC EPIDERMAL NECROLYSIS IN BRITAIN [J].
LYELL, A .
BRITISH JOURNAL OF DERMATOLOGY, 1967, 79 (12) :662-&
[10]   STAPHYLOCOCCAL SCALDED SKIN SYNDROME - EXPANDED CLINICAL SYNDROME [J].
MELISH, ME ;
GLASGOW, LA .
JOURNAL OF PEDIATRICS, 1971, 78 (06) :958-+