A GENETIC-DEFECT IN THE BINDING OF PROTEIN 4.1 TO SPECTRIN IN A KINDRED WITH HEREDITARY SPHEROCYTOSIS

被引:127
作者
WOLFE, LC
JOHN, KM
FALCONE, JC
BYRNE, AM
LUX, SE
机构
[1] SIDNEY FARBER CANC INST,BOSTON,MA 02115
[2] HARVARD UNIV,SCH MED,DEPT PEDIAT,BOSTON,MA 02115
关键词
D O I
10.1056/NEJM198211253072203
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1367 / 1374
页数:8
相关论文
共 39 条
[1]   DEFICIENT RED-CELL SPECTRIN IN SEVERE, RECESSIVELY INHERITED SPHEROCYTOSIS [J].
AGRE, P ;
ORRINGER, EP ;
BENNETT, V .
NEW ENGLAND JOURNAL OF MEDICINE, 1982, 306 (19) :1155-1161
[2]  
ALLEN DW, 1977, BLOOD, V49, P113
[3]  
BENNETT V, 1980, J BIOL CHEM, V255, P6424
[4]  
BRENNER SL, 1980, J BIOL CHEM, V255, P1670
[5]  
COETZER T, 1982, BLOOD, V59, P900
[6]  
FEO CJ, 1980, NOUV REV FR HEMATOL, V22, P315
[7]  
GOODMAN SR, 1980, J BIOL CHEM, V255, P8082
[8]  
GOODMAN SR, 1982, BLOOD, V60, P772
[9]  
GOODMAN SR, 1981, J SUPRAMOL STRUCT S, V5, P131
[10]  
GREENQUIST AC, 1978, BLOOD, V51, P1149