IMMUNOELECTRON MICROSCOPIC LOCALIZATION OF DYSTROPHIN IN MYOFIBERS

被引:441
作者
WATKINS, SC
HOFFMAN, EP
SLAYTER, HS
KUNKEL, LM
机构
[1] HARVARD UNIV,SCH MED,BOSTON,MA 02115
[2] CHILDRENS HOSP MED CTR,DIV GENET,BOSTON,MA 02115
[3] CHILDRENS HOSP MED CTR,HOWARD HUGHES MED INST,BOSTON,MA 02115
关键词
D O I
10.1038/333863a0
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:863 / 866
页数:4
相关论文
共 20 条
  • [1] BONILLA E, IN PRESS CELL
  • [2] BULLFIELD G, 1984, P NATL ACAD SCI USA, V81, P1189
  • [3] MORPHOLOGICAL-CHANGES IN DYSTROPHIC MUSCLE
    CULLEN, MJ
    MASTAGLIA, FL
    [J]. BRITISH MEDICAL BULLETIN, 1980, 36 (02) : 145 - &
  • [4] ALPHA-ACTININS AND THE DMD PROTEIN CONTAIN SPECTRIN-LIKE REPEATS
    DAVISON, MD
    CRITCHLEY, DR
    [J]. CELL, 1988, 52 (02) : 159 - 160
  • [5] Eisenberg B. R., 2010, HDB PHYSL 10, P73
  • [6] ENGEL AG, 1986, MYOLOGY, P1185
  • [7] PROTEIN-SEQUENCE OF DMD GENE IS RELATED TO ACTIN-BINDING DOMAIN OF ALPHA-ACTININ
    HAMMONDS, RG
    [J]. CELL, 1987, 51 (01) : 1 - 1
  • [8] HOFFMAN EH, IN PRESS NEURON
  • [9] DYSTROPHIN - THE PROTEIN PRODUCT OF THE DUCHENNE MUSCULAR-DYSTROPHY LOCUS
    HOFFMAN, EP
    BROWN, RH
    KUNKEL, LM
    [J]. CELL, 1987, 51 (06) : 919 - 928
  • [10] CHARACTERIZATION OF DYSTROPHIN IN MUSCLE-BIOPSY SPECIMENS FROM PATIENTS WITH DUCHENNES OR BECKERS MUSCULAR-DYSTROPHY
    HOFFMAN, EP
    FISCHBECK, KH
    BROWN, RH
    JOHNSON, M
    MEDORI, R
    LOIKE, JD
    HARRIS, JB
    WATERSTON, R
    BROOKE, M
    SPECHT, L
    KUPSKY, W
    CHAMBERLAIN, J
    CASKEY, CT
    SHAPIRO, F
    KUNKEL, LM
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1988, 318 (21) : 1363 - 1368