IS THERE A THRESHOLD LEVEL OF FETAL HEMOGLOBIN THAT AMELIORATES MORBIDITY IN SICKLE-CELL-ANEMIA

被引:258
作者
POWARS, DR
WEISS, JN
CHAN, LS
SCHROEDER, WA
机构
[1] CALTECH,DIV CHEM & CHEM ENGN,PASADENA,CA 91125
[2] UNIV SO CALIF,SCH MED,DEPT PEDIAT,DIV HEMATOL ONCOL,LOS ANGELES,CA 90033
[3] UNIV SO CALIF,SCH MED,DEPT PREVENT MED,LOS ANGELES,CA 90033
关键词
D O I
10.1182/blood.V63.4.921.921
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:921 / 926
页数:6
相关论文
共 26 条
[1]  
BOYER SH, 1983, MAY WORKSH DEV THER
[2]  
BRIEHL RW, 1980, TEX REP BIOL MED, V40, P207
[3]   SICKLE-CELL ANEMIA AND TRAIT IN SOUTHERN INDIA - FURTHER-STUDIES [J].
BRITTENHAM, G ;
LOZOFF, B ;
HARRIS, JW ;
MAYSON, SM ;
MILLER, A ;
HUISMAN, THJ .
AMERICAN JOURNAL OF HEMATOLOGY, 1979, 6 (02) :107-123
[4]  
CHARACHE S, 1982, BLOOD S, V60, pA44
[5]   SICKLE-CELL-ANEMIA - MOLECULAR AND CELLULAR BASES OF THERAPEUTIC APPROACHES .1. [J].
DEAN, J ;
SCHECHTER, AN .
NEW ENGLAND JOURNAL OF MEDICINE, 1978, 299 (14) :752-763
[6]   5-AZACYTIDINE STIMULATES FETAL HEMOGLOBIN-SYNTHESIS IN ANEMIC BABOONS [J].
DESIMONE, J ;
HELLER, P ;
HALL, L ;
ZWIERS, D .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (14) :4428-4431
[7]   INDIVIDUAL VARIATION IN PRODUCTION AND SURVIVAL OF F-CELLS IN SICKLE-CELL DISEASE [J].
DOVER, GJ ;
BOYER, SH ;
CHARACHE, S ;
HEINTZELMAN, K .
NEW ENGLAND JOURNAL OF MEDICINE, 1978, 299 (26) :1428-1435
[8]   F-CELL PRODUCTION IN SICKLE-CELL-ANEMIA - REGULATION BY GENES LINKED TO BETA-HEMOGLOBIN LOCUS [J].
DOVER, GJ ;
BOYER, SH ;
PEMBREY, ME .
SCIENCE, 1981, 211 (4489) :1441-1444
[9]  
DOVER GJ, 1983, MAY WORKSH DEV THER
[10]   SICKLE BETA-THALASSEMIA - IDENTICAL-TWINS DIFFERING IN SEVERITY IMPLICATE NONGENETIC FACTORS INFLUENCING COURSE [J].
JOISHY, SK ;
GRINER, PF ;
ROWLEY, PT .
AMERICAN JOURNAL OF HEMATOLOGY, 1976, 1 (01) :23-33