MARFAN-SYNDROME - DEMONSTRATION OF ABNORMAL ELASTIN IN AORTA

被引:68
作者
ABRAHAM, PA
PEREJDA, AJ
CARNES, WH
UITTO, J
机构
[1] UNIV CALIF LOS ANGELES, SCH MED, DEPT PATHOL, LOS ANGELES, CA 90024 USA
[2] UNIV CALIF LOS ANGELES, LOS ANGELES CTY HARBOR MED CTR, DIV DERMATOL, TORRANCE, CA 90509 USA
关键词
D O I
10.1172/JCI110723
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1245 / 1252
页数:8
相关论文
共 32 条
[1]   A MODIFIED URONIC ACID CARBAZOLE REACTION [J].
BITTER, T ;
MUIR, HM .
ANALYTICAL BIOCHEMISTRY, 1962, 4 (04) :330-&
[2]   STRUCTURALLY DISTINCT COLLAGEN TYPES [J].
BORNSTEIN, P ;
SAGE, H .
ANNUAL REVIEW OF BIOCHEMISTRY, 1980, 49 :957-1003
[3]   THE MARFAN-SYNDROME - A DEFICIENCY IN CHEMICALLY STABLE COLLAGEN CROSS-LINKS [J].
BOUCEK, RJ ;
NOBLE, NL ;
GUNJASMITH, Z ;
BUTLER, WT .
NEW ENGLAND JOURNAL OF MEDICINE, 1981, 305 (17) :988-991
[4]   MARFAN-SYNDROME - ABNORMAL ALPHA-2 CHAIN IN TYPE-I COLLAGEN [J].
BYERS, PH ;
SIEGEL, RC ;
PETERSON, KE ;
ROWE, DW ;
HOLBROOK, KA ;
SMITH, LT ;
CHANG, YH ;
FU, JCC .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1981, 78 (12) :7745-7749
[5]  
DEROUETTE S, 1981, PATHOL BIOL, V29, P537
[6]   SYNTHESIS OF CONNECTIVE-TISSUE PROTEIN IN SMOOTH-MUSCLE CELLS [J].
FARIS, B ;
SALCEDO, LL ;
COOK, V ;
JOHNSON, L ;
FOSTER, JA ;
FRANZBLAU, C .
BIOCHIMICA ET BIOPHYSICA ACTA, 1976, 418 (01) :93-103
[7]   URINARY-EXCRETION OF ELASTIN PEPTIDES CONTAINING DESMOSINE AFTER INTRA-TRACHEAL INJECTION OF ELASTASE IN HAMSTERS [J].
GOLDSTEIN, RA ;
STARCHER, BC .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 61 (05) :1286-1290
[8]   DESMOSINES IN HUMAN-URINE - AMOUNTS IN EARLY DEVELOPMENT AND IN MARFANS-SYNDROME [J].
GUNJASMITH, Z ;
BOUCEK, RJ .
BIOCHEMICAL JOURNAL, 1981, 193 (03) :915-918
[9]   DETERMINATION OF THE RELATIVE AMOUNTS OF ELASTIN IN LUNG TISSUES [J].
KELLER, S ;
MANDL, I ;
TURINO, GM .
BIOCHEMICAL MEDICINE, 1981, 25 (01) :74-80
[10]  
Kivirikko K I, 1970, Int Rev Connect Tissue Res, V5, P93