NEUROBLASTOMA-ASSOCIATED OPSOCLONAS-MYOCLONUS TREATED WITH INTRAVENOUSLY ADMINISTERED IMMUNE GLOBULIN-G

被引:43
作者
PETRUZZI, MJ
DEALARCON, PA
机构
[1] STATE UNIV NEW YORK BUFFALO, NEW YORK, NY USA
[2] UNIV VIRGINIA, MED CTR, DEPT PEDIAT, CHARLOTTESVILLE, VA USA
关键词
D O I
10.1016/S0022-3476(95)70322-5
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
An 18-month-old black girl had progressive truncal ataxia, opsoclonus, and multifocal myoclonus associated with a nonresectable abdominal ganglioneuroblastoma, Before chemotherapy, she received intravenously administered IgG, 1 gm/kg, for 2 days; within 48 hours of the first dose, there was significant improvement of the opsoclonus-myoclonus and ataxia, She required a 1 gm/kg maintenance dose every 4 to 6 weeks for a total of 12 doses, but is now free of symptomatic after 2 years with no therapy.
引用
收藏
页码:328 / 329
页数:2
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