CYSTIC-FIBROSIS PRESENTING AS KWASHIORKOR WITH FLORID SKIN RASH

被引：34

作者：

PHILLIPS, RJ ^{[1
]}

CROCK, CM ^{[1
]}

DILLON, MJ ^{[1
]}

CLAYTON, PT ^{[1
]}

CURRAN, A ^{[1
]}

HARPER, JI ^{[1
]}

机构：

[1] HOSP SICK CHILDREN, LONDON WC1N 3JH, ENGLAND

来源：

ARCHIVES OF DISEASE IN CHILDHOOD | 1993年 / 69卷 / 04期

关键词：

D O I：

10.1136/adc.69.4.446

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Two infants with a florid erythematous rash and generalised oedema, hypoalbuminaema, and anaemia were found to have cystic fibrosis. This rare presentation is associated with false negative sweat tests, delays in diagnosis, and a considerable mortality. It is proposed that this presentation represents a manifestation of kwashiorkor secondary to malabsorption. The recognition that these infants have kwashiorkor provides some insight into the pathogenesis and management of their illness.

引用

页码：446 / 448

页数：3

共 26 条

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