SURAL NERVE BIOPSY STUDIES IN LEIGH SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY

被引:35
作者
GOEBEL, HH
BARDOSI, A
FRIEDE, RL
KOHLSCHUTTER, A
ALBANI, M
SIEMES, H
机构
[1] UNIV GOTTINGEN,DEPT NEUROPATHOL,D-3400 GOTTINGEN,FED REP GER
[2] UNIV HAMBURG,DEPT PEDIAT,D-2000 HAMBURG 13,FED REP GER
[3] RUHR UNIV BOCHUM,DEPT PEDIAT,D-4630 BOCHUM,FED REP GER
关键词
D O I
10.1002/mus.880090210
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:165 / 173
页数:9
相关论文
共 27 条
[1]   A NEW APPROACH TOWARD ANALYZING PERIPHERAL-NERVE FIBER POPULATIONS .2. FORESHORTENING OF REGENERATED INTERNODES CORRESPONDS TO REDUCED SHEATH THICKNESS [J].
BEUCHE, W ;
FRIEDE, RL .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1985, 44 (01) :73-84
[2]   LEIGHS SUBACUTE NECROTIZING ENCEPHALOPATHY - CLINICAL AND BIOCHEMICAL STUDY WITH SPECIAL REFERENCE TO THERAPY WITH LIPOATE [J].
CLAYTON, BE ;
DOBBS, RH ;
PATRICK, AD .
ARCHIVES OF DISEASE IN CHILDHOOD, 1967, 42 (225) :467-+
[3]   EXPERIENCE WITH PHOSPHORYL TRANSFERASE INHIBITION IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY [J].
COOPER, JR ;
PINCUS, JH ;
ITOKAWA, Y ;
PIROS, K .
NEW ENGLAND JOURNAL OF MEDICINE, 1970, 283 (15) :793-&
[4]   RAGGED-RED FIBERS IN LEIGHS DISEASE [J].
CROSBY, TW ;
CHOU, SM .
NEUROLOGY, 1974, 24 (01) :49-54
[5]   DEFECTIVE ACTIVATION OF THE PYRUVATE-DEHYDROGENASE COMPLEX IN SUB-ACUTE NECROTIZING ENCEPHALOMYELOPATHY (LEIGH DISEASE) [J].
DEVIVO, DC ;
HAYMOND, MW ;
OBERT, KA ;
NELSON, JS ;
PAGLIARA, AS .
ANNALS OF NEUROLOGY, 1979, 6 (06) :483-494
[6]  
DUNN HG, 1969, NEUROLOGY MINNEAP, V19, P538
[7]   ACETAZOLAMIDE IN TREATMENT OF PYRUVATE DYSMETABOLISM SYNDROMES [J].
EVANS, OB ;
KILROY, AW ;
FENICHEL, GM .
ARCHIVES OF NEUROLOGY, 1978, 35 (05) :302-305
[8]   PYRUVATE DECARBOXYLASE DEFICIENCY IN SUB-ACUTE NECROTIZING ENCEPHALOMYELOPATHY [J].
EVANS, OB .
ARCHIVES OF NEUROLOGY, 1981, 38 (08) :515-519
[9]  
EVANS OB, 1979, PEDIATRICS, V64, P96
[10]   COMBINED SCATTER DIAGRAMS OF SHEATH THICKNESS AND FIBER CALIBER IN HUMAN SURAL NERVES - CHANGES WITH AGE AND NEUROPATHY [J].
FRIEDE, RL ;
BEUCHE, W .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1985, 48 (08) :749-756