DIFFERENTIAL DEGRADATION OF [S-35] METHIONINE POLYPEPTIDES IN DUCHENNE MUSCULAR-DYSTROPHY SKIN FIBROBLASTS INVITRO

被引:34
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RODEMANN, HP
BAYREUTHER, K
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10.1073/pnas.83.7.2086
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O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
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页码:2086 / 2090
页数:5
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共 38 条
[1]  
APPEL SH, 1978, METABOLIC BASIS INHE, P1260
[2]   INCREASED TURNOVER OF MUSCLE CONTRACTILE PROTEINS IN DUCHENNE MUSCULAR-DYSTROPHY AS ASSESSED BY 3-METHYLHISTIDINE AND CREATININE EXCRETION [J].
BALLARD, FJ ;
TOMAS, FM ;
STERN, LM .
CLINICAL SCIENCE, 1979, 56 (04) :347-352
[3]   FILM DETECTION METHOD FOR TRITIUM-LABELED PROTEINS AND NUCLEIC-ACIDS IN POLYACRYLAMIDE GELS [J].
BONNER, WM ;
LASKEY, RA .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1974, 46 (01) :83-88
[4]   DECREASE IN THE RATE OF PROTEIN-SYNTHESIS BY POLYSOMES FROM CULTURED FIBROBLASTS OF PATIENTS AND CARRIERS WITH DUCHENNE MUSCULAR-DYSTROPHY [J].
BOULE, M ;
VANASSE, M ;
BRAKIERGINGRAS, L .
CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES, 1979, 6 (03) :355-358
[5]  
BRAVO R, 1982, CLIN CHEM, V28, P766
[6]  
BRAVO R, 1984, 2 DIMENSIONAL GEL EL, P4
[7]   ANALYSIS OF SKIN FIBROBLAST PROTEINS IN DUCHENNE MUSCULAR-DYSTROPHY .1. SODIUM DODECYL-SULFATE POLYACRYLAMIDE-GEL ELECTROPHORESIS [J].
BURGHES, AHM ;
DUNN, MJ ;
STATHAM, HE ;
DUBOWITZ, V .
ELECTROPHORESIS, 1982, 3 (04) :177-185
[8]  
ETTIENNE EM, 1981, J BIOL CHEM, V256, P6408
[9]   DEFECTIVE CA-2+ METABOLISM IN DUCHENNE MUSCULAR-DYSTROPHY - EFFECTS ON CELLULAR AND VIRAL GROWTH [J].
FINGERMAN, E ;
CAMPISI, J ;
PARDEE, AB .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (23) :7617-7621
[10]   DECREASED LYSOSOMAL DIPEPTIDYL AMINOPEPTIDASE-I ACTIVITY IN CULTURED HUMAN-SKIN FIBROBLASTS IN DUCHENNES MUSCULAR-DYSTROPHY [J].
GELMAN, BB ;
PAPA, L ;
DAVIS, MH ;
GRUENSTEIN, E .
JOURNAL OF CLINICAL INVESTIGATION, 1980, 65 (06) :1398-1406