SERUM GRANULOCYTE COLONY-STIMULATING FACTOR LEVELS IN CHRONIC NEUTROPENIA OF INFANCY

被引:14
作者
MIZUNO, Y
HARA, T
NAGATA, M
OMORI, F
SHIMODA, K
OKAMURA, S
NIHO, Y
UEDA, K
机构
[1] KYUSHU UNIV,FAC MED,CTR CANC,DEPT PEDIAT,3-1-1 MAIDASHI,HIGASHI KU,FUKUOKA 812,JAPAN
[2] KYUSHU UNIV,DEPT INTERNAL MED 1,FUKUOKA 812,JAPAN
关键词
Autoimmune neutropenia; Congenital agranulocytosis; Granulocyte colony-stimulating factor;
D O I
10.3109/08880019009033415
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Eight infants with chronic neutropenia ranging in age from 1 to 13 months were studied for serum granulocyte colony-stimulating factor (G-CSF) levels. Serum G-CSF levels were elevated, especially when peripheral blood absolute neutrophil counts (ANC) were under 500/μl in seven patients with autoimmune neutropenia. On the other hand, in a patient with congenital agranulocytosis (Kostmann type), G-CSF levels were below the sensitivity of the assay (<50 pg/ml) despite severe neutropenia (<100/μl). © 1990 Informa UK Ltd All rights reserved: reproduction in whole or part not permitted.
引用
收藏
页码:377 / 381
页数:5
相关论文
共 10 条
  • [1] EFFECTS OF RECOMBINANT HUMAN GRANULOCYTE COLONY-STIMULATING FACTOR ON NEUTROPENIA IN PATIENTS WITH CONGENITAL AGRANULOCYTOSIS
    BONILLA, MA
    GILLIO, AP
    RUGGEIRO, M
    KERNAN, NA
    BROCHSTEIN, JA
    ABBOUD, M
    FUMAGALLI, L
    VINCENT, M
    GABRILOVE, JL
    WELTE, K
    SOUZA, LM
    OREILLY, RJ
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1989, 320 (24) : 1574 - 1580
  • [2] HEMATOPOIETIC GROWTH-FACTORS - BIOLOGY AND CLINICAL-APPLICATIONS
    GROOPMAN, JE
    MOLINA, JM
    SCADDEN, DT
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1989, 321 (21) : 1449 - 1459
  • [3] TREATMENT OF CYCLIC NEUTROPENIA WITH GRANULOCYTE COLONY-STIMULATING FACTOR
    HAMMOND, WP
    PRICE, TH
    SOUZA, LM
    DALE, DC
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1989, 320 (20) : 1306 - 1311
  • [4] INFANTILE GENETIC AGRANULOCYTOSIS - REVIEW WITH PRESENTATION OF 10 NEW CASES
    KOSTMANN, R
    [J]. ACTA PAEDIATRICA SCANDINAVICA, 1975, 64 (02): : 362 - 368
  • [5] AUTOIMMUNE NEUTROPENIA OF INFANCY
    LALEZARI, P
    KHORSHIDI, M
    PETROSOVA, M
    [J]. JOURNAL OF PEDIATRICS, 1986, 109 (05) : 764 - 769
  • [6] LALEZARI P, 1980, MANUAL CLIN IMMUNOLO, P744
  • [7] CLASSIFICATION OF CHRONIC GRANULOMATOUS-DISEASE ON THE BASIS OF MONOCLONAL-ANTIBODY DEFINED SURFACE CYTOCHROME-B DEFICIENCY
    MIZUNO, Y
    HARA, T
    NAKAMURA, M
    UEDA, K
    MINAKAMI, S
    TAKE, H
    [J]. JOURNAL OF PEDIATRICS, 1988, 113 (03) : 458 - 462
  • [8] MEASUREMENT OF HUMAN G-CSF BY ENZYME-LINKED IMMUNOSORBENT-ASSAY USING MONOCLONAL-ANTIBODY
    OMORI, F
    OKAMURA, S
    TAKAKU, F
    NIHO, Y
    [J]. RESEARCH IN EXPERIMENTAL MEDICINE, 1989, 189 (03) : 163 - 171
  • [9] TANIGUCHI S, 1989, ACTA HAEMATOL JPN, V52, P224
  • [10] WATARI K, 1989, BLOOD, V73, P117