EXERCISE INTOLERANCE, LACTIC-ACIDOSIS, AND ABNORMAL CARDIOPULMONARY REGULATION IN EXERCISE ASSOCIATED WITH ADULT SKELETAL-MUSCLE CYTOCHROME-C OXIDASE DEFICIENCY

被引:90
作者
HALLER, RG
LEWIS, SF
ESTABROOK, RW
DIMAURO, S
SERVIDEI, S
FOSTER, DW
机构
[1] VET ADM MED CTR, DEPT PHYSIOL, DALLAS, TX 75216 USA
[2] VET ADM MED CTR, DEPT BIOCHEM, DALLAS, TX 75216 USA
[3] VET ADM MED CTR, DEPT INTERNAL MED, DALLAS, TX 75216 USA
[4] COLUMBIA UNIV COLL PHYS & SURG, DEPT NEUROL, NEW YORK, NY 10032 USA
[5] UNIV TEXAS, SW MED CTR, DALLAS, TX 75235 USA
关键词
D O I
10.1172/JCI114135
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:155 / 161
页数:7
相关论文
共 56 条
  • [1] CYTOCHROME-C-OXIDASE DEFICIENCY IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY
    ARTS, WFM
    SCHOLTE, HR
    LOONEN, MCB
    PRZYREMBEL, H
    FERNANDES, J
    TRIJBELS, JMF
    LUYTHOUWEN, IEM
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 1987, 77 (01) : 103 - 115
  • [2] MEASUREMENT OF CYTOCHROMES IN HUMAN SKELETAL-MUSCLE MITOCHONDRIA, ISOLATED FROM FRESH AND FROZEN STORED MUSCLE SPECIMENS
    BOOKELMAN, H
    TRIJBELS, JMF
    SENGERS, RCA
    JANSSEN, AJM
    [J]. BIOCHEMICAL MEDICINE, 1978, 19 (03): : 366 - 373
  • [3] BRAUNWALD E, 1976, MECHANISMS CONTRACTI
  • [4] FATAL INFANTILE CYTOCHROME-C OXIDASE DEFICIENCY - DECREASE OF IMMUNOLOGICALLY DETECTABLE ENZYME IN MUSCLE
    BRESOLIN, N
    ZEVIANI, M
    BONILLA, E
    MILLER, RH
    LEECH, RW
    SHANSKE, S
    NAKAGAWA, M
    DIMAURO, S
    [J]. NEUROLOGY, 1985, 35 (06) : 802 - 812
  • [5] APPLICATIONS OF P-31-NMR TO CLINICAL BIOCHEMISTRY
    CHANCE, B
    [J]. ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1984, 428 (JUN) : 318 - 332
  • [6] DIMAURO S, 1986, ANN NY ACAD SCI, V488, P19
  • [7] CYTOCHROME-C-OXIDASE DEFICIENCY IN LEIGH SYNDROME
    DIMAURO, S
    SERVIDEI, S
    ZEVIANI, M
    DIROCCO, M
    DEVIVO, DC
    DIDONATO, S
    UZIEL, G
    BERRY, K
    HOGANSON, G
    JOHNSEN, SD
    JOHNSON, PC
    [J]. ANNALS OF NEUROLOGY, 1987, 22 (04) : 498 - 506
  • [8] MITOCHONDRIAL MYOPATHIES
    DIMAURO, S
    BONILLA, E
    ZEVIANI, M
    NAKAGAWA, M
    DEVIVO, DC
    [J]. ANNALS OF NEUROLOGY, 1985, 17 (06) : 521 - 538
  • [9] EDWARDS RHT, 1982, DISORDERS MOTOR UNIT, P715
  • [10] EXERCISE HYPERPNEA AND LOCOMOTION - PARALLEL ACTIVATION FROM THE HYPOTHALAMUS
    ELDRIDGE, FL
    MILLHORN, DE
    WALDROP, TG
    [J]. SCIENCE, 1981, 211 (4484) : 844 - 846