FATAL LACTIC ACIDOSIS IN A NEWBORN ATTRIBUTABLE TO A CONGENITAL DEFECT OF PYRUVATE-DEHYDROGENASE

被引:72
作者
STROMME, JH
BORUD, O
MOE, PJ
机构
[1] UNIV TROMSO,DEPT CLIN CHEM,TROMSO,NORWAY
[2] UNIV TROMSO,DEPT PEDIAT,TROMSO,NORWAY
关键词
D O I
10.1203/00006450-197601000-00012
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:60 / 66
页数:7
相关论文
共 39 条
[1]  
ANTENER I, 1969, Z KLIN CHEM KLIN BIO, V7, P427
[2]   STUDY OF PLASMA FREE AMINO-ACID LEVELS .2. NORMAL VALUES FOR CHILDREN AND ADULTS [J].
ARMSTRONG, MD ;
STAVE, U .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1973, 22 (04) :561-569
[3]  
BAERLOCHER K, 1971, HELV PAEDIATR ACTA, V26, P489
[4]  
BAKER L, 1970, LANCET, V2, P13
[5]  
BLASS J P, 1970, Journal of Clinical Investigation, V49, P423, DOI 10.1172/JCI106251
[6]   INHERITED DEFECT AFFECTING TRICARBOXYLIC ACID CYCLE IN A PATIENT WITH CONGENITAL LACTIC ACIDOSIS [J].
BLASS, JP ;
SCHULMAN, JD ;
YOUNG, DS ;
HOM, E .
JOURNAL OF CLINICAL INVESTIGATION, 1972, 51 (07) :1845-&
[7]  
BLASS JP, 1971, LANCET, V1, P1302
[8]  
BORUD O, IN PRESS
[9]  
BRODEHL J, 1968, PEDIATRICS, V42, P395
[10]   ACTIVITY OF PYRUVATE-DEHYDROGENASE IN RAT-BRAIN DURING POSTNATAL-DEVELOPMENT [J].
CREMER, JE ;
TEAL, HM .
FEBS LETTERS, 1974, 39 (01) :17-20