SENSITIVITY TO CARBOHYDRATE IN A PATIENT WITH FAMILIAL INTERMITTENT LACTIC-ACIDOSIS AND PYRUVATE-DEHYDROGENASE DEFICIENCY

被引：73

作者：

CEDERBAUM, SD

BLASS, JP

MINKOFF, N

BROWN, WJ

COTTON, ME

HARRIS, SH

机构：

[1] UNIV CALIF LOS ANGELES,SCH MED,MENTAL RETARDATION RES CTR,LOS ANGELES,CA 90024

[2] UNIV CALIF LOS ANGELES,SCH MED,DEPT PSYCHIAT,LOS ANGELES,CA 90024

[3] UNIV CALIF LOS ANGELES,SCH MED,DEPT PEDIAT,LOS ANGELES,CA 90024

[4] UNIV CALIF LOS ANGELES,SCH MED,DEPT BIOCHEM,LOS ANGELES,CA 90024

[5] UNIV CALIF LOS ANGELES,SCH MED,DEPT PATHOL,LOS ANGELES,CA 90024

来源：

PEDIATRIC RESEARCH | 1976年 / 10卷 / 08期

关键词：

D O I：

10.1203/00006450-197610080-00002

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：713 / 720

页数：8

共 38 条

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[6] INHERITED DEFECT AFFECTING TRICARBOXYLIC ACID CYCLE IN A PATIENT WITH CONGENITAL LACTIC ACIDOSIS [J].

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HOM, E .

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[9]

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[10]

BROWN RE, 1972, ARCH PATHOL, V94, P192

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