ADRENAL MYELOLIPOMA ASSOCIATED WITH CONGENITAL ADRENAL 21-HYDROXYLASE DEFICIENCY

被引：32

作者：

MURAKAMI, C ^{[1
]}

ISHIBASHI, M ^{[1
]}

KONDO, M ^{[1
]}

OHSHIRO, S ^{[1
]}

FUJITA, M ^{[1
]}

SATO, S ^{[1
]}

KAKO, M ^{[1
]}

FURUE, H ^{[1
]}

MIZUGUCHI, K ^{[1
]}

YAMAJI, T ^{[1
]}

机构：

[1] TEIKYO UNIV,SCH MED,DEPT MED 4,74 MIZONOKUCHI,TAKATSU KU,KAWASAKI 213,JAPAN

来源：

INTERNAL MEDICINE | 1992年 / 31卷 / 06期

关键词：

EXTRAADRENAL MYELOLIPOMA; CONGENITAL ADRENAL HYPERPLASIA; ACTH;

D O I：

10.2169/internalmedicine.31.803

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The occurrence of adrenal myelolipomas is reported in an untreated patient with congenital adrenal 21-hydroxylase deficiency. Laparotomy demonstrated the presence of two lesions, a large tumor which arose from an ectopic adrenal cortex and a smaller tumor in the left adrenal gland. Six cases of adrenal myelolipomas and congenital adrenal hyperplasia have been reported in the literature. All patients were associated with excessive ACTH secretion for a long period of time. The relative frequency of this association, coupled with the observation by Selye and Stone (Am J Pathol 26:211, 1950) that anterior pituitary extracts cause myelolipomatous changes in rats, may indicate a possible role for ACTH in the development of myelolipomas.

引用

页码：803 / 806

页数：4

共 15 条

[1]

Plaut A., Myelolipoma in the adrenal cortex, Am J Pathol, 34, (1958)

[2]

Olsson C.A., Krane R.J., Klugo R.C., Selikowitz S.M., Adrenal myelolipoma, Surgery, 73, (1973)

[3]

New M.I., Lorenzen F., Lerner A.J., Et al., Genotyping steroid 21-hydroxylase deficiency: hormonal reference data, J Clin Endocrinol Metab, 57, (1983)

[4]

Musante F., Derchi L.E., Zappasodi F., Et al., Myelolipoma of the adrenal gland: Sonographic and CT features, Am J Roentgenol, 15, (1988)

[5]

Schindler H., Myelolipom der Nebenniere bei adrenogenitalem Syndrom, Wien Med Wochenschr, 125, (1975)

[6]

Boudreaux D., Waisman J., Skinner D.G., Low R., Giant adrenal myelolipoma and testicular interstitial cell tumor in a man with congenital 21-hydroxylase deficiency, Am J Surg Pathol, 3, (1979)

[7]

Barr A.B., Giltman L.I., Congenital adrenal hyperplasia diagnosed in an 82-year-old: Case report, Virginia Med, 109, (1982)

[8]

Oliva A., Duarte B., Hammadeh R., Ghosh L., Baker R.J., Myelolipoma and endocrine function, Surgery, 103, (1988)

[9]

Miyazaki Y., Yoshida M., Doi J., A case of adrenal myelolipoma associated with adrenogenital syndrome, Acta Urol Jpn, 36, (1990)

[10]

Condom E., Villabona C.M., Gomez J.M., Varrera M., Adrenal myelolipoma in a woman with congenital 17-hydroxylase deficiency, Arch Pathol Lab Med, 109, (1985)

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