ELECTRON-BEAM THERAPY IN SCLEREDEMA ADULTORUM WITH ASSOCIATED MONOCLONAL HYPERGAMMAGLOBULINEMIA

被引:40
作者
ANGELIBESSON, C [1 ]
KOEPPEL, MC [1 ]
JACQUET, P [1 ]
ANDRAC, L [1 ]
SAYAG, J [1 ]
机构
[1] CHU TIMONE, DEPT ANATOMOPATHOL, F-13385 MARSEILLE 05, FRANCE
关键词
D O I
10.1111/j.1365-2133.1994.tb02940.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
We report a case of scleredema adultorum (Buschke's disease) associated with an IgA kappa monoclonal hypergammaglobulinaemia. A significant improvement in the skin was obtained with electron-beam therapy. Scleredema would appear to be linked to monoclonal hypergammaglobulinaemia, but the relationship between the skin disorder and the immunoglobulin abnormality remains to be elucidated.
引用
收藏
页码:394 / 397
页数:4
相关论文
共 21 条
[1]  
ANGELIBESSON C, 1992, THESIS MARSEILLE
[2]  
BUSCHKE A, ARCH DERMATOL SYPHIL, V53, P383
[3]   BUSCHKES SCLEREDEMA AND MONOCLONAL GAMMOPATHY - REPORT OF 3 CASES [J].
CLERICI, T ;
FAURE, M ;
CHOUVET, B ;
PERROT, H ;
HERMIER, C .
DERMATOLOGICA, 1983, 166 (05) :240-246
[4]   SCLEREDEMA - A HISTOCHEMICAL AND BIOCHEMICAL STUDY [J].
FLEISCHM.R ;
LARA, JV .
ARCHIVES OF DERMATOLOGY, 1965, 92 (06) :643-+
[5]   SCLEREDEMA ADULTORUM ASSOCIATED WITH IGG-KAPPA MULTIPLE-MYELOMA - A CASE-REPORT AND REVIEW OF THE LITERATURE [J].
HODAK, E ;
TAMIR, R ;
DAVID, M ;
HART, M ;
SANDBANK, M ;
PICK, A .
CLINICAL AND EXPERIMENTAL DERMATOLOGY, 1988, 13 (04) :271-274
[6]  
JABLONSKA S, 1972, DERMATOLOGICA, V144, P257
[7]   SCLEREDEMA ADULTORUM AND MULTIPLE-MYELOMA [J].
KORTING, GW ;
GILFRICH, HJ ;
MEYERZUM. .
ARCHIV FUR DERMATOLOGISCHE FORSCHUNG, 1974, 248 (04) :379-385
[8]   MONOCLONAL GAMMOPATHY IN SCLEREDEMA - OBSERVATIONS IN 3 CASES [J].
KOVARY, PM ;
VAKILZADEH, F ;
MACHER, E ;
ZAUN, H ;
MERK, H ;
GOERZ, G .
ARCHIVES OF DERMATOLOGY, 1981, 117 (09) :536-539
[9]  
LAZCANO FJS, 1984, REV CLIN ESP, V175, P245
[10]   ELECTRON-BEAM TREATMENT OF SCLEROMYXEDEMA [J].
LOWE, NJ ;
DUFTON, PA ;
HUNTER, RD ;
VICKERS, CFH .
BRITISH JOURNAL OF DERMATOLOGY, 1982, 106 (04) :449-453